Tus Sau: Lewis Jackson
Hnub Kev Tsim: 7 Tau 2021
Hloov Hnub: 1 Lub Xya Hli Ntuj 2024
Anonim
Idiopathic Pulmonary Fibrosis - pathophysiology, signs and symptoms, investigation and treatment
Daim Duab: Idiopathic Pulmonary Fibrosis - pathophysiology, signs and symptoms, investigation and treatment

Zoo Siab

Pulmonary fibrosis yog ib qho mob uas ua rau mob ntsws thiab txhav. Qhov no ua rau nws ua pa nyuaj. Nws tuaj yeem tiv thaiv koj lub cev los ntawm cov pa oxygen txaus thiab thaum kawg nws yuav ua rau lub ntsws ua pa, lub plawv tsis ua haujlwm, lossis lwm yam teebmeem.

Cov kws tshawb nrhiav tam sim no ntseeg hais tias kev sib xyaw ua ke ntawm kev cuam tshuam rau mob ntsws zoo li qee yam tshuaj lom neeg, haus luam yeeb, thiab kis tau tus mob, nrog rau cov noob caj noob ces thiab lub cev tiv thaiv kab mob, ua si lub luag haujlwm tseem ceeb hauv ntsws ntsws.

Nws tau xav txog ib zaug tias qhov mob yog los ntawm kev mob o. Tam sim no cov kws tshawb fawb ntseeg tias muaj cov txheej txheem kho mob hauv lub ntsws uas ua rau mob caws pliav. Qhov tsim los ntawm qhov tseem ceeb hauv kev mob ntsws thaum kawg ua rau mob ntsws.

Dab tsi yog mob ntsws pulmonary fibrosis?

Koj yuav muaj mob ntsws rau qee lub sijhawm tsis muaj tsos mob dab tsi. Ua pa luv feem ntau yog thawj cov tsos mob tshwm sim.

Lwm cov tsos mob tuaj yeem suav nrog:

  • qhuav, hacking hnoos uas mob ntev (ntev ntev)
  • tsis muaj zog
  • nkees
  • curving ntawm cov rau tes, uas hu ua clubbing
  • poob phaus
  • lub hauv siab tsis xis nyob

Txij li thaum tus mob feem ntau cuam tshuam rau cov neeg laus zog, cov tsos mob thaum ntxov feem ntau misattributed rau lub hnub nyoog lossis tsis muaj kev tawm dag zog.


Koj cov tsos mob yuav zoo li tseem me thaum xub thawj thiab nce qib tom ntej. Cov tsos mob tuaj yeem sib txawv ntawm ib tus neeg mus rau lwm tus. Qee cov neeg mob ntsws ntsig ua rau mob sai sai.

Dab tsi ua rau mob ntsws ntsig?

Qhov ua rau ntawm lub ntsws cov hlab ntsws tuaj yeem muab faib ua ntau pawg:

  • cov kab mob autoimmune
  • kis tau tus mob
  • ib puag ncig raug
  • tshuaj noj
  • idiopathic (tsis paub)
  • noob caj noob ces

Cov kab mob autoimmune

Cov kab mob autoimmune ua rau koj lub cev tiv thaiv kab mob tawm tsam nws tus kheej. Qhov mob autoimmune uas tuaj yeem ua rau mob txhaws ntswg xws li:

  • rheumatoid mob caj dab
  • lupus erythematosus, uas feem ntau hu ua lupus
  • scleroderma
  • polymyositis
  • dermatomyositis
  • vasculitis

Kab mob

Cov kab mob hauv qab no tuaj yeem ua rau mob ntsws ntsig:

  • cov kab mob sib kis
  • virual voos xwm txheej, tshwm sim los ntawm kab mob siab C, adenovirus, tus kab mob pob sawv hlwv, thiab lwm yam kab mob

Ib puag ncig raug

Raug rau cov khoom hauv ib puag ncig lossis chaw ua haujlwm kuj tseem tuaj yeem pab ua rau cov hlab ntsws. Piv txwv li, cov pa luam yeeb muaj ntau yam chemical uas tuaj yeem ua rau koj lub ntsws mob thiab ua rau tus mob no.


Lwm yam uas tuaj yeem ua rau koj lub ntsws muaj:

  • asbestos fibers
  • nplej hmoov av
  • silica hmoov av
  • tej roj cua
  • hluav taws xob

Cov Tshuaj Kho Mob

Qee cov tshuaj kuj tseem tuaj yeem ua rau koj qhov kev pheej hmoo ntawm kev tsim muaj cov hlab ntsws ntsws. Yog tias koj noj ib qho ntawm cov tshuaj no tsis tu ncua, koj yuav tsum tau saib xyuas los ntawm koj tus kws kho mob.

  • Siv tshuaj khomob, xws li cyclophosphamide
  • cov tshuaj tua kab mob, xws li nitrofurantoin (Macrobid) thiab sulfasalazine (Azulfidine)
  • tshuaj mob plawv, xws li amiodarone (Nexterone)
  • cov tshuaj biologic xws li adalimumab (Humira) los yog etanercept (Enbrel)

Idiopathic

Feem ntau, qhov tseeb ua rau mob ntsws ntsig tsis paub meej. Thaum qhov xwm txheej no, qhov mob hu ua idiopathic pulmonary fibrosis (IPF).

Raws li American Lub Koom Haum Lub ntsws, feem ntau cov neeg muaj ntsws txhaws muaj IPF.

Noob caj noob ces

Raws li Pulmonary Fibrosis Foundation, kwv yees li 3 txog 20 feem pua ​​ntawm cov neeg nrog IPF muaj lwm tus neeg hauv tsev neeg uas muaj mob ntsws pulmonary fibrosis. Hauv cov xwm txheej no, nws tau paub tias mob ntsws ntsig los yog mob ntsws.


Cov kws tshawb nrhiav tau txuas qee cov noob keeb rau tus mob, thiab kev tshawb fawb txog dab tsi lub luag haujlwm hauv noob caj noob ces.

Puas muaj leej twg pheej hmoo mob ntsws ntsws?

Koj yuav ntxim yuav raug ntsuas mob ntsws ntsws yog tias koj:

  • yog txiv neej
  • yog cov muaj hnub nyoog 40 thiab 70
  • muaj keeb kwm ntawm kev haus luam yeeb
  • muaj tsev neeg muaj keeb kwm ntawm tus mob
  • muaj lub autoimmune cuam tshuam nrog tus mob
  • tau noj qee yam tshuaj cuam tshuam nrog tus kabmob
  • tau txais kev kho mob cancer, tshwj xeeb tshaj plaws hauv siab
  • ua haujlwm hauv ib txoj haujlwm ua rau cuam tshuam nrog kev pheej hmoo ntau ntxiv, xws li kev khawb av, kev ua liaj ua teb, lossis kev tsim vaj tsev

Yuav kuaj li cas thiaj mob ntsws ntsws?

Pulmonary fibrosis yog ib ntawm ntau dua 200 hom mob ntsws uas muaj nyob. Vim tias nws muaj ntau ntau hom kab mob ntsws, koj tus kws kho mob yuav muaj teeb meem los txheeb xyuas seb puas mob ntsws txoj hlab ntsws yog qhov ua rau koj cov tsos mob.

Hauv kev sojntsuam los ntawm Pulmonary Fibrosis Foundation, 55 feem pua ​​ntawm cov neeg teb tau qhia raug ntsuas qee yam. Cov kev soj ntsuam uas tsis zoo tshaj plaws yog hawb pob, mob ntsws, thiab mob ntsws.

Siv cov lus qhia tam sim no, kwv yees tias 2 nyob rau 3 tus neeg mob ntsws ntsws tam sim no tuaj yeem kuaj tau yam tsis muaj kev soj ntsuam me me.

Los ntawm kev sib txuas nrog koj cov ntaub ntawv kho mob thiab cov txiaj ntsig ntawm ib hom CT scan ntawm lub hauv siab, koj tus kws kho mob yuav txheeb xyuas qhov tseeb rau koj.

Hauv qee kis thaum kev kuaj mob tsis meej, cov ntaub so ntswg cov ntaub so ntswg, lossis kuaj me me, yuav tsim nyog.

Muaj ntau txoj hauv kev los ua kev phais mob ntsws, yog li koj tus kws kho mob yuav pom zoo rau cov txheej txheem twg uas zoo tshaj rau koj.

Koj tus kws kho mob kuj tseem yuav siv ntau yam cuab yeej los tshuaj rau kev mob ntsws ntsig los yog txiav txim lwm yam mob. Cov no suav nrog:

  • mem tes oximetry, ib qho kev kuaj tsis yooj yim ntawm koj cov ntshav cov ntshav
  • kuaj ntshav mus saib tus kab mob autoimmune, kab mob thiab ntshav liab
  • kev ntsuam xyuas cov roj ntsha cov ntshav feem ntau ntsuas cov pa oxygen hauv koj cov ntshav
  • qauv hnoos qeev los kuaj seb puas muaj tus kab mob
  • kev kuaj mob ntsws ntsig ntsuas seb koj lub ntsws ua li cas
  • ib daim tawv nqaij echocardiogram lossis kev kuaj xyuas kev ntxhov siab kom pom tias lub plawv puas ua rau koj cov tsos mob

Yuav kho tus mob ntsws ntsws li cas?

Koj tus kws kho mob tsis tuaj yeem hloov kho txoj kev mob ntsws, tab sis lawv tuaj yeem sau ntawv kho mob los pab ua kom koj ua pa zoo thiab ua kom qeeb qeeb ntawm kev mob.

Cov kev kho mob hauv qab no yog qee cov piv txwv ntawm cov kev xaiv tam sim no siv rau kev tswj hwm cov hlab ntsws:

  • ntxiv pa oxygen
  • prednisone los mus tiv thaiv koj lub cev tsis muaj zog thiab txo qhov mob
  • azathioprine (Imuran) lossis mycophenolate (CellCept) txhawm rau tiv thaiv koj lub cev tsis muaj zog
  • pirfenidone (Esbriet) lossis nintedanib (Ofev), cov tshuaj tua kabmob uas thaiv qhov kev ua haujlwm hauv txoj hlab ntsws

Koj tus kws kho mob kuj tseem yuav pom zoo kom rov zoo mob ntsws. Cov kev kho no koom nrog ib qho kev tawm dag zog, kev kawm, thiab kev txhawb nqa los pab koj kawm ua pa yooj yim dua.

Koj tus kws kho mob kuj tseem tuaj yeem txhawb koj kom hloov pauv mus rau hauv koj lub neej. Cov kev pauv no yuav muaj xws li hauv qab no:

  • Koj yuav tsum zam kev haus luam yeeb thiab taug kev txiav luam yeeb yog koj haus luam yeeb. Qhov no tuaj yeem pab ua kom tus mob qeeb zuj zus thiab ua rau koj ua pa yooj yim.
  • Noj zaub mov kom zoo rau lub cev.
  • Ua raws li cov kev tawm dag zog tau tsim nrog koj tus kws kho mob cov lus qhia.
  • So kom txaus thiab zam dhau kev ntxhov siab ntau.

Kev pom zoo rau lub ntsws yuav tsum raug pom zoo rau cov neeg muaj hnub nyoog 65 xyoos uas muaj kab mob hnyav.

Dab tsi yog qhov kev xam pom rau cov neeg mob ntsws ntsws?

Tus nqi uas mob ntsws ntsig ua rau neeg lub ntsws lub ntsws txawv. Qhov caws pliav tsis tuaj yeem thim rov qab, tab sis koj tus kws kho mob tuaj yeem pom zoo cov kev kho mob kom txo tus nqi uas koj tus mob nce.

Tus mob no tuaj yeem ua rau ntau yam kev cuam tshuam, nrog rau kev ua pa tsis ua haujlwm. Qhov no tshwm sim thaum koj lub ntsws tsis ua haujlwm zoo thiab lawv tsis tuaj yeem muaj oxygen txaus rau koj cov ntshav.

Kev mob ntsws pulmonary kuj tseem yuav ua rau koj muaj feem mob ntsws.

Cov lus qhia txog kev tiv thaiv

Qee qhov mob ntsig txog txoj hlab ntsws (pulmonary fibrosis) tsis tuaj yeem tiv thaiv. Lwm qhov xwm txheej tau cuam tshuam nrog ib puag ncig thiab kev coj tus cwj pwm pheej hmoo uas tuaj yeem tswj tau. Ua raws li cov lus qhia no txhawm rau txo qhov kev pheej hmoo kis tus mob:

  • Zam kev haus luam yeeb.
  • Zam kev haus luam yeeb ua pa.
  • Looj ntaub npog ntsej muag lossis lwm yam khoom ua pa yog tias koj ua haujlwm nyob rau hauv ib puag ncig nrog tshuaj lom neeg.

Yog tias koj muaj teeb meem ua pa, teem caij nrog koj tus kws kho mob. Kev paub ntxov thiab kev kho tuaj yeem txhim kho txoj kev xav kom ntev rau cov neeg muaj kab mob ntsws, nrog rau cov hlab ntsws.

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