Ob chav aortic koov

Ob chav aortic yog ib qho txawv txav ntawm lub aorta, cov hlab ntsha loj uas nqa ntshav los ntawm lub plawv mus rau lwm qhov ntawm lub cev. Nws yog ib qho teeb meem kev tsis sib xws, txhais tau tias nws yog thaum yug.

Ob chav aortic daim pib yog ib qho kev sib koom ua ke ntawm ib pawg ntawm qhov tsis xws luag uas cuam tshuam rau txoj kev loj hlob ntawm aorta hauv niam plab. Cov kev tsis zoo no ua rau lub cev tsis meej hu ua viav vias voos ntiv nplhaib (cov voj voos ntawm cov hlab ntshav).

Feem ntau, aorta txhim kho los ntawm ib qho ntawm ob peb daim nkhaus ntawm cov nqaij (arches). Raws li cov menyuam mos pib loj hlob hauv lub tsev menyuam, cov hneev hle tau faib ua ntau ntu. Lub cev zom qee lub hneev, thaum lwm tus tsim ua txoj hlab ntshav. Aorta uas nquag tau tsim yog ib daim ntawv tshaj tawm uas tawm hauv lub siab thiab txav mus sab laug.

Hauv ob chav aortic, qee cov hneev uas yuav tsum tau ploj mus yog tseem muaj thaum yug ntxiv nrog rau lub koov. Cov menyuam mos uas muaj ob lub aortic arch muaj ib qho aorta uas tau ua los ntawm ob lub nkoj hloov ntawm ib qho.Ob ntu mus rau aorta muaj cov hlab ntsha me ua haujlwm tawm ntawm lawv. Yog li ntawd, ob ceg tuaj ib ncig thiab nias kom txoj hlab pas thiab txoj hlab (hlab pas) uas nqa zaub mov los ntawm lub qhov ncauj mus rau lub plab.

Ob lub aortic koov yuav tshwm sim hauv lwm qhov tsis xws lub plawv, nrog rau:

• Tetralogy ntawm Fallot
• Truncus txoj hlab ntsha
• Kev Hloov ntawm txoj hlab ntshav loj
• Ventricular septal teem meem

Ob chav aortic koov yog qhov tsis tshua muaj heev. Vascular rings ua kom muaj feem pua ​​me me ntawm tag nrho cov teeb meem mob lub plawv. Ntawm cov no, me ntsis ntau dua li ib nrab yog tshwm sim los ntawm ob aortic koov. Tus mob no muaj sib npaug hauv txivneej thiab pojniam. Feem ntau nws tshwm sim rau cov neeg uas muaj qee qhov kev qoos chromosome.

Vim tias cov tsos mob ntawm ob aortic koov feem ntau me me, qhov teeb meem yuav tsis pom mus txog thaum tus me nyuam muaj ob peb xyoos.

Ob chav aortic yuav nias ntawm lub pob zom thiab txoj hlab pas, ua rau muaj teeb meem ua pa thiab nqos. Qhov hnyav ntawm cov tsos mob nyob ntawm ntau npaum li cas aortic koov tau nias rau cov qauv no.

Cov mob ua pa xws li:

• Lub suab muaj suab nrov thaum lub caij ua pa (stridor)
• Ua pa nrov
• Rov mob ntsws dua
• Hawb pob

Digestive cov tsos mob yuav muaj xws li:

• Txhawm chim
• Nyuaj noj thiab nqos
• Ntuav

Cov tsos mob yuav ua rau tus kws saib xyuas kev noj qab haus huv xav tias muaj ob lub aortic arch. Lwm txoj kev kuaj mob ntxiv yuav tsum tau los teev cov kev kuaj mob.

Cov ntawv sim hauv qab no tuaj yeem pab txheeb xyuas ob chav aortic:

• Kev ntsuas hluav taws xob xoo
• Cov kev soj ntsuam uas tsim cov duab uas muaj ob ntu ntawm lub cev (CT lossis MRI scan)
• Ultrasound kev tshuaj xyuas ntawm lub plawv (echocardiography)
• Xoo hluav taws xob uas siv cov tshuaj uas qhia txog txoj hlab pas (barium nqos)

Cov kev phais tuaj yeem kho ua tiav ob chav aortic. Tus kws phais mob txuas nrog cov ceg me thiab nws cais tawm ntawm cov ceg loj. Tom qab ntawd tus kws phais mob kaw lub qhov kawg ntawm aorta nrog stitches. Qhov no daws qhov siab ntawm txoj hlab pas thiab txoj hlab pa.

Feem ntau cov menyuam yaus tau zoo nyob tom qab kev phais mob, txawm tias qee tus yuav muaj cov tsos mob ua pa rau qee lub sijhawm tom qab phais mob tas. Qhov no feem ntau vim yog lub cev tsis muaj zog vim tias lub zog ntawm nws ua ntej kev phais mob.

Muaj qee zaus, yog tias tus koov tawm ntawm tus pa nyuaj heev, tus menyuam yuav ua pa nyuaj uas ua rau tuag taus.

Teeb meem yuav suav nrog:

• Ua tsis tiav
• Kab mob sib kis
• Hnav kom deb ntawm daim tawv nqaij txoj hlab pas (txoj hlab nqos mov) thiab txoj hlab pas
• Tsis tshua muaj neeg, muaj kev sib txuas tsis meej ntawm txoj hlab pas thiab aorta (aortoesophageal fistula)

Hu rau koj tus kws kho mob yog tias koj tus menyuam mos liab muaj mob ob npaug aortic arch.

Kuj tsis muaj txoj hauv kev los tiv thaiv tus mob no.

Aortic koov anomaly; Ob chav koov; Congenital plawv tsis zoo - ob chav aortic; Kev yug tus me nyuam lub plawv - ob npaug aortic koov

• Hlaus nplhaib
• Ob chav aortic koov

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Fraser CD, Kane LC. Congenital mob plawv. Hauv: Townsend CM Jr, Beauchamp RD, Evers BM, Mattox KL, eds. Sabiston Phau Ntawv Txog Kev Kho MobCov. 20 tus ed. Philadelphia, PA: Elsevier; 2017: chap 58.

Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM. Lwm qhov ua haujlwm tsis zoo ntawm lub plawv thiab vascular. Hauv: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Phau Ntawv ntawm PediatricsCov. 21st ed. Philadelphia, PA: Elsevier; 2020: chap 459.

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