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An Overview of Hereditary Haemorrhagic Telangiectasia (HHT) by Prof Claire Shovlin
Daim Duab: An Overview of Hereditary Haemorrhagic Telangiectasia (HHT) by Prof Claire Shovlin

Telangiectasias yog cov me me, nthuav cov hlab ntshav ntawm daim tawv nqaij. Lawv feem ntau tsis muaj mob, tab sis tuaj yeem cuam tshuam nrog ntau yam kab mob.

Telangiectasias tuaj yeem tsim nyob txhua qhov chaw hauv lub cev. Tab sis lawv pom tau yooj yim tshaj plaws ntawm daim tawv nqaij, cov leeg thiab lub ntsej muag thiab lub ntsej muag dawb. Feem ntau, lawv tsis ua kom muaj tsos mob. Qee qhov telangiectasias los ntshav thiab ua rau muaj teeb meem loj. Telangiectasias kuj tseem tuaj yeem tshwm sim hauv lub hlwb lossis cov hnyuv thiab ua rau muaj teeb meem loj los ntawm los ntshav.

Cov ua yuav suav nrog:

  • Rosacea (teeb meem ntawm daim tawv nqaij uas ua rau lub ntsej muag tig liab)
  • Laus
  • Teeb meem cov noob
  • Cev xeeb tub
  • Hnub raug
  • Varicose leeg
  • Ntau dhau ntawm cov tshuaj steroid
  • Kev poob plig rau thaj chaw

Cov kab mob cuam tshuam nrog cov mob no suav nrog:

  • Ataxia-telangiectasia (kab mob uas cuam tshuam rau daim tawv nqaij, sib npaug thiab kev sib koom tes, thiab lwm qhov chaw ntawm lub cev)
  • Cov tsos mob tawg paj (cov kab mob muaj keeb uas ua rau lub cev luv, ua kom tawv nqaij tiv thaiv duab tshav ntuj, thiab ua ntsej muag liab)
  • Cutis marmorata telangiectatica congenita (mob tawv nqaij ua rau thaj chaw muaj liab)
  • Kab mob los ntshav keeb (Osler-Weber-Rendu syndrome)
  • Klippel-Trenaunay-Weber syndrome (kab mob uas ua rau chaw nres nkoj caw, cov leeg ua pa, thiab cov leeg nqaij muaj teeb meem)
  • Nevus flammeus xws li chaw nres nkoj-caw tsuas
  • Rosacea (mob tawv nqaij uas ua rau lub ntsej muag liab)
  • Kab mob Sturge-Weber (kab mob uas txuam nrog chaw nres nkoj caw qaug thiab teeb meem lub paj hlwb)
  • Xeroderma pigmentosa (kab mob uas ua rau tawv nqaij thiab tawv nqaij npog lub qhov muag yog qhov tsis tshua muaj kev pom txog kev tiv thaiv cov teeb ci ci ultraviolet)
  • Lupus (mob tiv thaiv kab mob)
  • CREST syndrome (hom mob scleroderma uas cuam tshuam nrog tsim cov caws pliav zoo li daim tawv nqaij thiab lwm qhov hauv lub cev thiab ua rau cov hlwb ua rau txoj hlab ntshav me)

Hu rau koj tus kws kho mob yog tias koj pom cov hlab ntsha hauv daim tawv nqaij, nqaij mos, lossis qhov muag.


Tus kws khomob yuav kuaj ib ce thiab nug txog koj cov tsos mob, suav nrog:

  • Cov hlab ntshav nyob qhov twg?
  • Lawv puas los ntshav yooj yim thiab tsis muaj laj thawj?
  • Lwm tus mob dab tsi tshwm sim?

Tej zaum yuav tau coj mus kuaj lossis kho mob kom dhau. Kev ntsuam xyuas yuav muaj xws li:

  • Kuaj ntshav
  • CT scans
  • Kev tshawb fawb lub siab ua haujlwm
  • MRI scans
  • Kev xoo hluav taws xob

Sclerotherapy yog kev kho mob rau telangiectasias ntawm txhais ceg. Hauv cov txheej txheem no, cov tshuaj tov ntsev (ntsev) lossis lwm yam tshuaj lom neeg yuav txhaj ncaj qha rau cov leeg kab laug sab ntawm ob txhais ceg. Kev kho mob laser feem ntau yog siv los kho telangiectasias ntawm lub ntsej muag.

Vascular ectasias; Kab laug sab angioma

  • Angioma serpiginosum
  • Telangiectasia - txhais ceg
  • Telangiectasias - sab caj npab

Kelly R, Baker C. Lwm yam kev mob vascular. Hauv: Bolognia JL, Schaffer JV, Cerroni L, eds. Lub cev ntaj ntsugCov. 4 tug ed. Philadelphia, PA: Elsevier; 2018: chap 106.


Patterson JW. Leeg hlav hlav. Hauv: Patterson JW, ed. Weedon's Cov Khoom Siv Tawv TawvCov. 4 tug ed. Philadelphia, PA: Elsevier Churchill Livingstone; 2016: chap 38.

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