Tus Sau: William Ramirez
Hnub Kev Tsim: 24 Lub Cuaj Hli Ntuj 2021
Hloov Hnub: 1 Lub Xya Hli Ntuj 2024
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12.Clinical Live Teaching : Hereditary Motor Sensory Neuropathy
Daim Duab: 12.Clinical Live Teaching : Hereditary Motor Sensory Neuropathy

Sensorimotor polyneuropathy yog ib qho mob uas ua rau lub peev xwm txav qis los sis txav mus los (hnov) vim tias cov leeg puas.

Neuropathy txhais tau tias yog ib tus kab mob ntawm, lossis kev puas tsuaj rau cov leeg. Thaum nws tshwm sim sab nraud ntawm lub hauv nruab nrab cov hlab hlwb (CNS), uas yog, lub hlwb thiab tus txha caj qaum, nws hu ua peripheral neuropathy. Mononeuropathy txhais tau tias ib qho hlab ntsha koom tes nrog. Polyneuropathy txhais tau hais tias ntau txoj hlab ntshav hauv qhov chaw sib txawv ntawm lub cev tau koom nrog.

Neuropathy tuaj yeem cuam tshuam rau cov hlab ntsha uas muab qhov kev xav zoo siab (lub siab neuropathy) lossis ua rau lub zog (lub cev muaj zog neuropathy). Nws kuj tseem tuaj yeem cuam tshuam rau ob qho tib si, qhov no nws yog hu ua sensorimotor neuropathy.

Sensorimotor polyneuropathy yog lub cev thoob lub cev (txheej txheem) muaj kev puas tsuaj rau cov hlab hlwb, cov hlab ntsha (axons), thiab cov hlab npog (myelin sheath). Kev puas tsuaj rau lub vov ntawm cov hlab ntsha ua rau cov hlab ntsaws ua rau qeeb los yog nres. Kev puas tsuaj rau cov hlab ntaws lossis tag nrho cov xov paj ntawm lub paj hlwb tuaj yeem ua rau cov leeg ua haujlwm tsis zoo. Qee cov leeg mob hlwb loj hlob mus ntau xyoo, thaum lwm tus tuaj yeem pib thiab muaj mob hnyav li ib teev rau hnub.


Kev puas ntsoog tuaj yeem los ntawm:

  • Autoimmune (thaum lub cev tawm tsam nws tus kheej) cuam tshuam
  • Cov xwm txheej uas muab siab rau cov hlab ntshav leeg
  • Txo cov ntshav ntws mus rau txoj hlab ntaws
  • Cov kab mob uas ua rau cov kua nplaum puas tsuaj (cov ntaub so ntswg sib txuas) uas tuav cov hlwb thiab cov nqaij ua ke
  • O o (mob) ntawm qab haus huv

Qee cov kab mob ua rau mob polyneuropathy uas yog qhov hnov ​​mob lossis lub cev muaj zog. Cov teeb meem uas ua tau ntawm sensorimotor polyneuropathy muaj xws li:

  • Cawv mob neuropathy
  • Amyloid polyneuropathy
  • Cov kab mob autoimmune, xws li Sjögren syndrome
  • Mob Cancer (hu ua paraneoplastic neuropathy)
  • Ntev ntev (mob mus ntev) mob neuropathy
  • Mob neuropathy mob ntshav qab zib
  • Tshuaj neuropathy muaj feem xyuam nrog kev siv tshuaj kho mob
  • Guillain-Barré mob
  • Mob caj dab mob rau leeg
  • HIV / AIDS
  • Qes qes
  • Kab mob Parkinson
  • Muaj cov vitamins (cov vitamins B12, B1, thiab E)
  • Tus kab mob Zika kis tau

Cov tsos mob tuaj yeem suav nrog ib qho hauv qab no:


  • Txo kev xav nyob rau hauv ib cheeb tsam ntawm lub cev
  • Nyuaj nyuaj los nqos lossis ua pa
  • Nyuaj siv tes los yog tes
  • Nyuaj siv cov ceg lossis txhais taw
  • Kev taug kev nyuaj
  • Mob, kub hnyiab, ntxais tawm, los yog txawv txav hauv txhua qhov chaw ntawm lub cev (hu ua neuralgia)
  • Tsis muaj zog ntawm lub ntsej muag, caj npab, ceg lossis ib qho chaw ntawm lub cev
  • Qee zaus ntog vim tsis muaj qhov sib npaug thiab tsis hnov ​​hauv av hauv qab ntawm koj txhais taw

Cov tsos mob yuav pib sai sai (xws li hauv Guillain-Barré syndrome) lossis maj mam dhau ntau lub lim tiam mus rau xyoo. Cov tsos mob feem ntau tshwm sim rau ob sab ntawm lub cev. Feem ntau, lawv pib ntawm qhov kawg ntawm tus ntiv taw ua ntej.

Tus kws kho mob yuav kuaj xyuas koj thiab nug koj cov tsos mob. Ib qho kev xeem tuaj yeem qhia:

  • Tsis hnov ​​zoo lawm (tej zaum yuav cuam tshuam kev kov, qhov mob, kev co, lossis qhov ua rau hnov)
  • Txo reflexes (feem ntau cov pob luj taws)
  • Nqaij mob atrophy
  • Nqaij sib tw
  • Nqaij tsis muaj zog
  • Tuag tes tuag taw

Kev ntsuam xyuas yuav muaj xws li:


  • Txo tawm ntawm cov hlab ntsha cuam tshuam
  • Kuaj ntshav
  • Kev kuaj hluav taws xob ntawm cov leeg (EMG)
  • Hluav taws xob xeem ntawm cov hlab sib dhos
  • Cov duab xoo hluav taws xob lossis lwm yam kev sim duab, xws li MRI

Cov hom phiaj ntawm kev kho mob suav nrog:

  • Nrhiav tus ua
  • Tswj cov tsos mob
  • Txhawb nqa tus kheej txoj kev saib xyuas tus kheej thiab kev ywj pheej

Nyob ntawm qhov laj thawj, kev kho yuav suav nrog:

  • Hloov tshuaj, yog tias lawv tsim teeb meem
  • Tswj kev tswj ntshav qab zib kom ntshav qab zib, thaum lub paj hlwb yog mob ntshav qab zib
  • Tsis haus dej haus cawv
  • Noj tshuaj pab kom noj qab nyob zoo txhua hnub
  • Tshuaj kho mob los kho qhov pib qhov pib ntawm polyneuropathy

PROMOTING SELF-CARE THIAB INDEPENDENCE

  • Kev tawm dag zog thiab rov ua kom lub luag haujlwm ntawm lub qab haus huv uas puas lawm
  • Txoj haujlwm (kev kawm haujlwm) txoj kev kho
  • Kev Kho Mob Ua Haujlwm
  • Kev kho mob pob qij txha
  • Kev kho lub cev
  • Lub tog muaj log, kev zawm hniav, lossis kev faib tawm

TSWJ LWM NTAWM SYMPTOMS

Kev nyab xeeb yog qhov tseem ceeb rau cov neeg mob neuropathy. Tseem tsis leeg tswj hwm thiab tsis hnov ​​zoo siab tuaj yeem ua rau muaj kev pheej hmoo ntawm kev ntog lossis lwm yam kev raug mob.

Yog tias koj muaj teeb meem txav mus los, cov kev ntsuas no tuaj yeem pab koj kom ruaj ntseg:

  • Tso lub teeb rau.
  • Tshem cov teeb meem (xws li cov kab xoob uas yuav xoob hauv av).
  • Ntsuas dej kub ua ntej da dej.
  • Siv kev tsheb nqaj hlau.
  • Hnav cov khau tiv thaiv (xws li cov neeg uas muaj ntiv taw kaw thiab cov luj taws qis).
  • Rau khau uas tsis yog khau khiab.

Lwm cov lus qhia suav nrog:

  • Kuaj koj ob txhais taw (lossis lwm qhov cuam tshuam) txhua hnub rau qhov nqaij doog, qhib thaj chaw tawv nqaij, lossis lwm yam kev raug mob, uas koj yuav tsis pom thiab tuaj yeem kis kab mob tau.
  • Xyuas sab hauv ntawm khau rau ntau rau cov pob zeb lossis cov ntxhib uas yuav ua rau koj txhais taw mob.
  • Mus ntsib tus kws kho mob ko taw (tus kws kho pob ntseg) txhawm rau txhawm rau tshuaj xyuas thiab txo qis kev pheej hmoo ntawm kev raug mob rau koj txhais taw.
  • Tsis txhob khoov ntawm koj lub lauj tshib, hla koj lub hauv caug, lossis nyob rau lwm qhov chaw uas yuav ua rau mob siab rau qee qhov chaw ntawm lub cev.

Cov tshuaj siv los kho tus mob no:

  • Cov tshuaj yuav tom khw thiab kws kho mob muab tshuaj kom txo tau tus mob chob mob (neuralgia)
  • Anticonvulsants lossis tshuaj tiv thaiv kab mob
  • Zas pleev, pleev tshuaj, lossis pleev tshuaj rau

Siv tshuaj mob tsuas yog thaum tsim nyog. Ua kom koj lub cev tau nyob rau qhov yog lossis ua kom cov ntaub pua chaw pw tawm ntawm lub cev mos mos tuaj yeem pab tswj kev mob.

Cov pab pawg no tuaj yeem muab cov ntaub ntawv qhia ntxiv txog mob hlwb.

  • Neuropathy Action Foundation - www.neuropathyaction.org
  • Lub Hauv Paus rau Peripherial Neuropathy - www.foundationforpn.org

Muaj qee kis, koj tuaj yeem kho tau rov qab los ntawm tus mob neippathy yog tias koj tus kws kho mob tuaj yeem nrhiav qhov ua rau thiab ua tiav zoo, thiab yog tias qhov kev puas tsuaj tsis cuam tshuam rau tag nrho cov hlab ntsha.

Tus nqi ntawm kev tsis taus nws txawv. Qee cov neeg tsis xiam oob qhab. Lwm tus muaj qhov tsis paub txog ib nrab lossis ua tiav ntawm kev txav, ua haujlwm lossis hnov ​​zoo. Kev hnov ​​mob hauv plab yuav tsis xis nyob thiab yuav nyob ntev mus.

Qee qhov xwm txheej, sensorimotor polyneuropathy ua rau mob hnyav, tuag taus.

Cov teeb meem uas tuaj yeem tshwm sim suav nrog:

  • Kev sib txawv
  • Kev raug mob rau ko taw (tshwm sim los ntawm cov khau tsis zoo lossis dej kub thaum mus rau hauv lub dab da dej)
  • Looj
  • Mob
  • Taug kev taug kev
  • Neeg tsis muaj zog
  • Nyuaj ua pa lossis nqos (thaum mob hnyav)
  • Ntog vim tsis muaj qhov sib npaug

Hu rau koj tus kws kho mob yog tias koj muaj qhov ua xiam los yog mloog zoo nyob hauv ib qho ntawm koj lub cev. Kev paub kuaj ntxov thiab kho kab mob yuav muaj feem ntau tuaj yeem tswj hwm cov tsos mob.

Polyneuropathy - sensorimotor

  • Nruab nrab hauv lub paj hlwb thiab lub paj hlwb peripheral
  • Kev tswj hwm leeg

Craig A, Richardson JK, Ayyangar R. Rov kho cov neeg mob neuropathies. Hauv: Cifu DX, ed. Braddom Tshuaj Lub Cev & Lub Cev Kho Kom ZooCov. Thib 5 ed. Philadelphia, PA: Elsevier; 2016: chaaj 41.

Endrizzi SA, Rathmell JP, Hurley RW. Mob lub paj hlwb mob hlwb. Hauv: Benzon HT, Raja SN, Liu SS, Fishman SM, Cohen SP, eds. Qhov tseem ceeb ntawm Cov Tshuaj Kho MobCov. 4 tug ed. Philadelphia, PA: Elsevier; 2018: chap 32.

Katitji B. Kev mob tsis zoo ntawm cov hlab ntsha leeg. Hauv: Daroff RB, Jankovic J, Mazziotta JC, Pomeroy SL, eds. Bradley's Neurology nyob rau hauv Kev Soj NtsuamCov. 7 tus ed. Philadelphia, PA: Elsevier; 2016: chap 107.

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