Cov tsos mob Birt-Hogg-Dubé

Zoo Siab

• Cov duab ntawm Birt-Hogg-Dubé Syndrome
• Cov tsos mob ntawm Birt-Hogg-Dubé Syndrome
• Kev Kho Mob Birt-Hogg-Dubé Syndrome
• Cov kev sib txuas tseem ceeb:

Tus mob Birt-Hogg-Dubé Syndrome yog ib hom mob uas tsis tshua muaj mob caj ces ua rau tawv nqaij mob, mob raum thiab mob ua paug hauv lub ntsws.

Ntawm ua rau mob Birt-Hogg-Dubé Syndrome lawv yog kev sib pauv hauv cov gene ntawm cov keeb xoo 17, hu ua FLCN, uas plam nws txoj haujlwm ua lub qog ua kom hlav thiab coj mus ua kom pom cov qog hauv cov neeg.

LUB Cov mob Birt-Hogg-Dubé tsis muaj kev kho tau thiab nws txoj kev kho mob muaj tshem tawm cov qog thiab tiv thaiv lawv cov tsos.

Cov duab ntawm Birt-Hogg-Dubé Syndrome

Hauv cov duab koj tuaj yeem txheeb xyuas cov tawv nqaij uas tshwm sim hauv Birt-Hogg-Dubé Syndrome, uas ua rau muaj cov qog benign me uas tsim nyob ib ncig ntawm plaub hau.

Cov tsos mob ntawm Birt-Hogg-Dubé Syndrome

Cov tsos mob ntawm Birt-Hogg-Dubé Syndrome tuaj yeem yog:

• Benign cov qog ntawm daim tawv nqaij, mas ua ntsej muag, caj dab thiab hauv siab;
• Cov hlwv hlaws;
• Benign raum mob qog los yog mob raum;
• Lub ntsws pulmonary;
• Kev nkag mus ntawm huab cua ntawm lub ntsws thiab lub pleura, ua rau lub ntsej muag pneumothorax;
• Lub qog nodules.

Cov neeg muaj mob Birt-Hogg-Dubé Syndrome feem ntau yuav mob qog nqaij hlav cancer hauv lwm qhov chaw ntawm lub cev xws li lub mis, amygdala, lub ntsws lossis txoj hnyuv.

Qhov mob txhab uas tshwm rau ntawm daim tawv nqaij yog hu ua fibrofolliculomas thiab muaj pob ntxau me me uas los ntawm kev txuam nrog collagen thiab cov fibers nyob ib ncig ntawm plaub hau. Feem ntau, daim paib no rau ntawm daim tawv nqaij ntawm Birt-Hogg-Dubé Syndrome tshwm sim thaum muaj hnub nyoog 30 txog 40 xyoo.

O kuaj mob Birt-Hogg-Dubé Syndrome nws tau ua tiav los ntawm kev txheeb xyuas cov tsos mob ntawm tus kab mob thiab kev kuaj keeb kwm kom paub qhov kev hloov pauv hauv FLNC gene.

Kev Kho Mob Birt-Hogg-Dubé Syndrome

Kev kho mob ntawm Birt-Hogg-Dubé Syndrome tsis kho tus kab mob, tab sis nws pab txo nws cov tsos mob thiab rau lub neej ntawm cov tib neeg.

Benign hlav uas tshwm sim rau ntawm daim tawv nqaij tuaj yeem tshem tawm phais, dermo-ua puas, laser lossis tawv nqaij coj.

Mob raum nyob rau hauv lub raum lossis lub raum mob yuav tsum tiv thaiv los ntawm kev ua kom pom tom tom qab, cov khoom sib nqus los yog cov kev kuaj mob ultrasound. Yog tias qhov kuaj pom qog lossis qog ua haujlwm thaum kuaj, lawv yuav tsum raug phais.

Hauv qee kis uas mob qog noj qab nyob zoo, kev kho mob yuav tsum muaj kev phais mob, kho mob lossis hluav taws xob kho.

Cov kev sib txuas tseem ceeb:

• Raum raum
• Pneumothorax