Tus Sau: Christy White
Hnub Kev Tsim: 6 Tau 2021
Hloov Hnub: 25 Lub Rau Hlis Ntuj 2024
Anonim
Phenylketonuria - causes, symptoms, diagnosis, treatment, pathology
Daim Duab: Phenylketonuria - causes, symptoms, diagnosis, treatment, pathology

Zoo Siab

Phenylalanine tuaj yeem pab tswj cov hnyav dua vim tias nws koom nrog cov txheej txheem uas tswj kev noj zaub mov kom zoo thiab ua rau lub cev muaj qhov zoo siab. Phenylalanine yog ib qho amino acid uas tuaj yeem pom nyob rau hauv cov zaub mov muaj protein ntau, xws li nqaij, ntses thiab mis thiab khoom noj siv mis, thiab hauv cov tshuaj uas muag hauv khw muag tshuaj thiab cov khw muag khoom noj khoom haus huv.

Kev siv cov tshuaj phenylalanine yuav tsum yog kws kho mob lossis kws qhia zaub mov noj thiab yog siv rau cov neeg muaj teeb meem xws li kub siab, mob plawv thiab poj niam cev xeeb tub.

Kev ua ntawm phenylalanine ntawm kev tshaib plab tswj

Phenylalanine ua rau kev tswj kev tshaib kev nqhis vim nws koom nrog tsim dopamine thiab norepinephrine, tshuaj yog qhov tseem ceeb rau kev tswj hwm kev noj zaub mov thiab uas tseem koom nrog kev tswj hwm kev kawm, kev xav thiab cim xeeb. Tsis tas li ntawd, phenylalanine txhawb kev tsim khoom ntawm cholecystokinin hormone, uas ua rau hauv plab hnyuv thiab ua rau lub cev mloog zoo li tsis txaus siab.


Feem ntau koob pom zoo ntawm phenylalanine yog 1000 txog 2000 mg rau ib hnub, tab sis nws txawv raws li tus neeg tus yam ntxwv, xws li hnub nyoog, kev tawm dag zog thiab muaj cov teeb meem xws li kev ntxhov siab thiab ntxhov siab. Txawm li cas los xij, phenylalanine pab ntxiv ib leeg tsis txaus kom poob ceeb thawj, vim tias kev poob phaus tsuas yog tshwm sim thaum tseem muaj kev noj qab haus huv zoo.

Khoom noj muaj txiaj ntsig phenylalaninePhenylalanine ntxiv

Kev saib xyuas uas yuav tsum tau ua nrog phenylalanine ntxiv

Koj yuav tsum tau ceev faj nrog phenylalanine ntxiv vim tias qhov tshaj ntawm cov amino acid no tuaj yeem muaj cov kev mob tshwm sim xws li kub siab, xeev siab thiab mob taub hau. Phenylalanine tseem ua tiav qhov tsis txaus ntseeg ntawm:


  • Kab mob hauv lub plawv;
  • Tawg siab;
  • Cov poj niam cev xeeb tub lossis pub niam mis;
  • Cov neeg uas siv tshuaj los kho kev ntxhov siab lossis lwm yam kev puas siab ntsws;
  • Cov neeg muaj phenylketonuria.

Yog li, ntxiv rau phenylalanine yuav tsum tau coj los ntawm kws kho mob lossis tus neeg noj zaub mov kom paub meej nws cov txiaj ntsig zoo.

Khoom noj muaj txiaj ntsig phenylalanine

Phenylalanine yog ib txwm muaj nyob hauv cov zaub mov muaj protein ntau, xws li nqaij, ntses, mis thiab khoom noj siv mis, txiv ntoo, taum pauv, taum pauv thiab pob kws. Kev noj cov phenylalanine hauv kev noj haus tsis ua rau muaj kev phom sij rau kev noj qab haus huv thiab tsuas yog cov neeg muaj phenylketonuria yuav tsum zam cov zaub mov no. Saib daim ntawv ua tiav ntawm Phenylalanine-nplua nuj zaub mov.

Yog tias koj tab tom nrhiav kom poob ceeb thawj, saib ntxiv:

  • Lub cev yuag sai
  • Yuav ua li cas thiaj noj zaub mov tsis zoo rau koj lub cev

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