Pierre Robin sib lawv liag

Pierre Robin sib lawv liag (los yog qhov mob) yog ib qho mob uas cov menyuam mos muaj lub me dua li lub puab tsaig sab qis dua, tus nplaig uas poob rov rau hauv caj pas, thiab ua pa nyuaj. Nws yog tam sim no thaum yug los.

Vim li cas tiag Pierre Robin sib lawv liag tsis paub. Tej zaum nws yuav yog ib feem ntawm ntau cov cim caj ces.

Lub puab tsaig hauv qab yuav pib maj mam ua ntej yug, tab sis yuav loj hlob sai dua nyob rau thawj ob peb xyoos ntawm lub neej.

Cov tsos mob ntawm tus mob no suav nrog:

• Ciaj xim ntawm lub palate
• High-arched palate
• Lub puab tsaig uas yog qhov tsawg heev nrog lub puab tsaig me me
• Lub puab tsaig uas nyob deb kawg nkaus hauv caj pas
• Rov ua dua pob ntseg mob
• Qhib me me hauv lub ru tsev ntawm lub qhov ncauj, uas tuaj yeem ua rau daig caj pas lossis dej rov qab los ntawm lub qhov ntswg
• Cov hniav uas tshwm thaum tus menyuam yug los
• Nplaig uas loj dua piv rau lub puab tsaig

Tus kws saib xyuas kev noj qab haus huv feem ntau tuaj yeem kuaj tus mob no thaum lub sijhawm kuaj mob lub cev. Sab laj nrog tus kws kho mob caj ces tuaj yeem txiav txim tawm lwm yam teeb meem cuam tshuam nrog tus mob no.

Tham nrog koj tus menyuam tus kws kho mob txog kev pw nyab xeeb. Qee tus menyuam mos nrog Pierre-Robin sib lawv liag yuav tsum tau pw hauv lawv lub plab es tsis txhob ua lawv sab nraub qaum kom tiv thaiv lawv tus nplaig kom tsis txhob rov poob rau lawv txoj hlab pa.

Hauv cov xwm txheej hauv nruab nrab, tus menyuam yuav xav tau lub raj tso rau hauv lub qhov ntswg thiab nkag rau hauv cov pa kom tsis txhob txhaws cov hlab cua. Thaum muaj mob hnyav, yuav tsum tau phais txhawm rau txhawm rau txhaws cov hlab cua kom nrov. Qee tus menyuam yaus yuav tsum tau phais txhawm rau ua lub qhov nyob hauv lawv txoj hlab pa lossis txav lawv lub puab tsaig mus tom ntej.

Kev pub rau noj yuav tsum ua kom zoo kom tsis txhob daig thiab ua pa tawm ntawm cov pa. Tus menyuam yuav xav noj cov raj kom tiv thaiv txhawm chim.

Cov peev txheej hauv qab no tuaj yeem muab cov ntaub ntawv qhia ntxiv ntawm Pierre Robin kab ntawv:

• Kev Tshawb Nrhiav Menyuam Yug Me Nyuam Rau Cov Menyuam Yaus-www.birthdefects.org/pierre-robin-syndrome
• Lub Cleft Palate Foundation - www.cleftline.org
• Lub Koom Haum Hauv Tebchaws rau Cov Tsis Txaus Ntseeg --rarediseases.org/rare-diseases/pierre-robin-ntawm

Txhawm chim thiab pub teeb meem rau noj yuav ploj mus ntawm lawv tus kheej li thawj ob peb lub xyoo thaum cov puab tsaig hauv qab mus ua ib qho tsis xwm yeem. Muaj kev pheej hmoo siab rau teeb meem yog tias tus menyuam cov kev ua pa tsis ceev faj kom tsis txhob txhaws.

Cov teeb meem no tuaj yeem tshwm sim:

• Ua pa nyuaj, tshwj xeeb yog thaum tus me nyuam pw
• Zais hauv ntu
• Congestive lub plawv tsis ua haujlwm
• Kev Tuag
• Noj pub nyuaj
• Cov pa oxygen tsawg thiab lub hlwb puas (vim ua pa nyuaj)
• Hom ntshav siab hu ua pulmonary tawg

Cov menyuam mosliab uas yug los nrog tus mob no feem ntau kuaj pom thaum yug los.

Hu rau koj tus kws khomob yog koj tus menyuam hawb mob hawb pob lossis ua pa nyuaj. Qhov uas thaiv cov hlab cua ua pa yuav ua rau lub suab nrov thaum tus menyuam nqus pa. Nws tuaj yeem ua rau tawv nqaij tawv (ua paug).

Hu rau yog tias koj tus me nyuam muaj lwm cov teeb meem ua pa.

Tsis muaj kev paub txog kev tiv thaiv. Txoj kev kho yuav txo qhov teeb meem ua pa thiab txhawm chim.

Cov mob Pierre Robin; Pierre Robin txoj; Pierre Robin anomaly

• Tus menyuam mos tawv tawv thiab sab hauv

Dhar V. Syndromes nrog qhov ncauj tawm. Hauv: Kliegman RM, Stanton BF, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Phau Ntawv ntawm PediatricsCov. 21st ed. Philadelphia, PA: Elsevier; 2020: cha 337.

Purnell CA, Gosain AK. Pierre Robin sib lawv liag. Hauv: Rodriguez ED, Losee JE, Neligan PC, eds. Kev Phais Yas: Ntim Peb: Craniofacial, Taub Hau thiab Caj Dab Thiab Pediatric Yas HlaisCov. 4 tug ed. Philadelphia, PA: Elsevier; 2018: chap 36.