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Hereditary amyloidosis yog ib qho mob uas cov protein tsis txaus (hu ua amyloid) nyob rau hauv yuav luag txhua daim ntaub hauv lub cev. Kev tso nyiaj txaus ntshai feem ntau ua rau lub plawv, raum, thiab cov leeg hlab ntshav. Cov protein no ua kev puas tsuaj rau cov ntaub so ntswg thiab cuam tshuam nrog kev ua haujlwm ntawm cov nruab nrog.

Tus mob muaj keeb yog kis los ntawm niam txiv mus rau lawv cov me nyuam (cov muaj los tau). Cov noob kuj tseem tuaj yeem ua lub luag haujlwm tseem ceeb hauv amyloidosis.

Lwm yam kab mob amyloidosis yog tsis tau txais kabmob. Lawv suav nrog:

  • Senile systemic: pom hauv cov neeg laus dua 70 xyoo
  • Spontaneous: tshwm sim yam uas tsis muaj tus paub
  • Thib ob: los ntawm cov kab mob xws li mob cancer ntawm cov qe ntshav (myeloma)

Cov xwm txheej tshwj xeeb suav nrog:

  • Mob amyloidosis
  • Cerebral amyloidosis
  • Secondary systemic amyloidosis

Kev kho mob txhawm rau txhim kho txoj haujlwm ntawm cov plab hnyuv siab raum yuav pab txo qee cov tsos mob ntawm tus mob amyloidosis. Kev ua haujlwm rau lub siab yuav pab txo qis kev tsim cov amyloid protein tsis zoo. Tham nrog koj tus kws kho mob txog kev kho mob.


Amyloidosis - kev mob siab; Familial amyloidosis

  • Amyloidosis ntawm cov ntiv tes

Budd RC, Seldin DC. Mob Amyloidosis. Hauv: Firestein GS, Budd RC, Gabriel SE, McInnes IB, O'Dell JR, eds. Kelley thiab Firestein Cov Ntawv Phau Ntawv ntawm RheumatologyCov. 10 tus ed. Philadelphia, PA: Elsevier; 2017: chap 116.

Gertz MA. Mob Amyloidosis. Hauv: Goldman L, Schafer AI, eds. Goldman-Cecil TshuajCov. 26th ed. Philadelphia, PA: Elsevier; 2020: cha 179.

Hawkins PN. Mob Amyloidosis. Hauv: Hochberg MC, Gravallese EM, Silman AJ, Smolen JS, Weinblatt ME, Weisman MH, eds. Pob tsuasCov. 7 tus ed. Philadelphia, PA: Elsevier; 2019: chap 177.

Pom Zoo Los Ntawm Peb

12 Khw Muag Khw Muag Khw Koj Yuav Xav nyiag - Er, Qhia

12 Khw Muag Khw Muag Khw Koj Yuav Xav nyiag - Er, Qhia

Peb uav nrog cov khoom ua peb xav tia t eem ceeb rau peb cov nyeem. Yog tia koj yuav lo ntawm cov txua hauv nplooj ntawv no, peb yuav khwv tau nyiaj me me. Ntawm no yog peb cov txheej txheem.Cov menyu...
6 Cov Khoom Siv Rau Cov Khoom Siv Rau Cov Me Nyuam Mos

6 Cov Khoom Siv Rau Cov Khoom Siv Rau Cov Me Nyuam Mos

Peb uav nrog cov khoom ua peb xav tia t eem ceeb rau peb cov nyeem. Yog tia koj yuav lo ntawm cov txua hauv nplooj ntawv no, peb yuav khwv tau nyiaj me me. Ntawm no yog peb cov txheej txheem.Thaum koj...