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Mob ntsws pulmonary veno-occlusive - Tshuaj Kho Mob
Mob ntsws pulmonary veno-occlusive - Tshuaj Kho Mob

Mob ntsws pulmonary veno-occlusive (PVOD) yog ib yam kab mob uas tsis tshua muaj tshwm sim. Nws ua rau muaj ntshav siab ntxiv hauv cov hlab ntsws ntawm txoj hlab ntsws (mob ntsws).

Feem ntau, qhov ua rau PVOD tsis paub. Qhov ntshav siab tshwm sim hauv cov hlab ntsws cov hlab ntsws. Cov hlab ntsha ntsws no txuas ncaj qha rau sab xis ntawm lub plawv.

Qhov xwm txheej yuav cuam tshuam nrog kev kis tus kab mob. Nws yuav tshwm sim vim yog ib qho kev cuam tshuam ntawm qee yam kab mob xws li mob lupus, lossis hloov hlwb pob txha.

Qhov kev cuam tshuam no tshwm sim muaj ntau rau cov menyuam yaus thiab cov neeg hluas. Thaum tus kab mob zuj zus tuaj, nws ua rau:

  • Txoj hlab ntsws nqaim
  • Pulmonary leeg ntshav siab
  • Kev khoob thiab o tuaj ntawm lub ntsws

Cov kev pheej hmoo txaus ntshai rau PVOD suav nrog:

  • Tsev neeg keeb kwm ntawm qhov mob
  • Haus Yeeb
  • Raug cov tshuaj zoo li trichlorethylene lossis tshuaj khomob
  • Kab mob sclerosis (mob nruab nrog cev nqaij daim tawv)

Cov tsos mob tuaj yeem suav nrog ib qho hauv qab no:


  • Ua tsis taus pa
  • Qhuav hnoos
  • Qaug zog ntawm kev ntxaib
  • Tsaus muag
  • Kev hnoos ntshav
  • Ua pa nyuaj thaum dag tiaj

Tus kws kho mob yuav tshuaj xyuas koj thiab nug koj li keeb kwm kho mob thiab cov tsos mob.

Qhov kev kuaj mob yuav qhia:

  • Ntxiv zog hauv cov leeg leeg caj dab
  • Clubbing ntawm cov ntiv tes
  • Bluish coloration ntawm daim tawv nqaij vim tias tsis muaj oxygen (cyanosis)
  • O o hauv ceg

Koj tus kws kho mob yuav hnov ​​lub suab txawv txav thaum mloog lub hauv siab thiab lub ntsws nrog lub stethoscope.

Cov kev xeem hauv qab no tuaj yeem ua:

  • Arterial ntshav roj
  • Cov ntshav oximetry
  • Kev ntsuas hluav taws xob xoo
  • Chest CT
  • Txoj Kev Ntshaw Mob
  • Lub ntsws muaj nuj nqi kuaj
  • Echocardiogram
  • Lub ntsws me

Tamsis no tseem tsis tau muaj txoj kev khomob uas siv tau zoo. Txawm li cas los xij, cov tshuaj hauv qab no tuaj yeem pab rau qee tus neeg:

  • Cov tshuaj uas nthuav dav cov hlab ntsha (vasodilators)
  • Cov tshuaj uas tswj lub cev tiv thaiv kab mob (xws li azathioprine lossis steroids)

Tej zaum yuav muaj mob ntsws hloov.


Qhov tshwm sim feem ntau txom nyem heev hauv cov menyuam mos, nrog kev muaj sia nyob ntawm ob peb lub lis piam xwb. Ciaj sia nyob hauv cov neeg laus yuav yog lub hlis txog ob peb xyoos.

Teeb meem ntawm PVOD yuav suav nrog:

  • Ua pa nyuaj uas tuaj tsis zoo, suav nrog thaum hmo ntuj (pw tsaug zog ua pa)
  • Pulmonary tawg
  • Right-sided heart tsis ua hauj lwm (cor pulmonale)

Hu rau koj tus kws kho mob yog tias koj muaj cov tsos mob ntawm qhov tsis zoo no.

Mob ntsws pulmonary vaso-occlusive

  • Kev ua pa system

Kwv Txhiaj K, Channick RN. Pulmonary tawg. Hauv: Broaddus VC, Mason RJ, Ernst JD, li al, eds. Murray thiab Nadel Cov Ntawv Phau Ntawv Qhia Txog Cov PaCov. 6 tus ed.Philadelphia, PA: Elsevier Saunders; 2016: chap 58.

Churg A, Wright JL. Pulmonary tawg. Hauv: Leslie KO, Wick MR, eds. Tshaj Tawm Pulmonary Pathology: Ib Txoj Kev Ntsuas Kev Pom ZooCov. 3lawm ed. Philadelphia, PA: Elsevier; 2018: chap 12.


Mclaughlin VV, Humbert M. Pulmonary tawg. Hauv: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. Braunwald's Plawv Lub Plawv: Phau Ntawv Qhia Txog Cov Tshuaj Mob plawvCov. 11th ed. Philadelphia, PA: Elsevier; 2019: chap 85.

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