Yuav kho tus mob hemophilia li cas

Zoo Siab

• Hom kev kho mob
• Kev kho mob thaum mob hemophilia nrog tshuaj inhibitor
• Saib xyuas thaum kho

Kev kho tus mob hemophilia yog ua los ntawm kev hloov pauv txhaws txhaws rau qhov tsis txaus ntawm tus neeg, uas yog qhov xwm txheej VIII, nyob rau hauv rooj plaub ntawm hemophilia hom A, thiab yam IX, nyob rau hauv cov ntaub ntawv ntawm hemophilia hom B, raws li nws thiaj li tuaj yeem tiv thaiv. los ntshav ntau dhau.

Hemophilia yog ib hom kab mob caj ces uas ua rau txo qis kev ua si lossis tsis tuaj yeem ua rau ntshav txhaws, uas yog cov protein nyob rau hauv cov ntshav uas ua haujlwm thaum muaj cov hlab ntaws, tiv thaiv kom ntshav ntau dhau. Yog li, thaum ua qhov siv ntawm qhov hloov pauv txhawm rau txhawm rau, nws muaj peev xwm ua rau tus neeg mob hemophilia ua lub neej zoo, tsis muaj kev txwv ntau. Kawm ntxiv txog hemophilia.

Hom kev kho mob

Txawm hais tias tsis muaj kev kho kom zoo, kev kho tshuaj hemophilia pab tiv thaiv kom tsis txhob los ntshav los ntawm kev nquag tshwm sim, thiab yuav tsum tau coj los ntawm hematologist thiab tuaj yeem ua ob txoj kev sib txawv:

• Kev tiv thaiv kev kho mob: muaj cov kev hloov pauv txhua zaus, kom lawv ib txwm hloov siab ntau hauv lub cev, thiab tiv thaiv kom tsis txhob los ntshav. Hom kev kho no tej zaum yuav tsis tsim nyog yog tias muaj mob me ntsis, thiab nws yuav raug pom zoo kom ua qhov kev kho mob tsuas yog thaum muaj qee yam mob hemorrhage.
• Kev kho mob tom qab los ntshav: nws yog kev kho mob rau kev thov, ua tiav txhua qhov teeb meem, nrog daim ntawv thov ntawm qhov txhaws khov kho thaum muaj qhov rov los ntshav, uas tso cai rau nws daws sai dua.

Hauv ib qho ntawm cov kev kho mob, koob tshuaj yuav tsum tau muab xam raws qhov hnyav hauv lub cev, qhov mob hnyav ntawm hemophilia thiab cov ntshav txhaws ntawm theem uas txhua tus neeg muaj nyob hauv lawv cov ntshav. Qhov Ntsuas VIII lossis IX cov khoom siv nrog cov hmoov ampoule uas yog diluted nrog cov dej distilled rau daim ntawv thov.

Ntxiv rau, lwm yam ntawm cov neeg sawv cev hemostatic siv tau los pab hauv kev coagulation, xws li cryoprecipitate, prothrombin complex thiab desmopressin, piv txwv. Cov kev kho no tau ua yam tsis raug them nqi los ntawm SUS, hauv lub xeev cov chaw hematology, tsuas yog raug xa mus los ntawm cov kws kho mob tshwj xeeb lossis hematologist.

Kev kho mob thaum mob hemophilia nrog tshuaj inhibitor

Qee qhov hemophiliacs tuaj yeem tsim cov tshuaj tiv thaiv tawm tsam qhov sib txawv VIII lossis IX concentrate siv rau kev kho mob, hu ua inhibitors, uas tuaj yeem ua rau tsis zoo rau cov lus teb kho mob.

Hauv cov rooj plaub no, nws yuav tsim nyog nqa tawm kev kho mob nrog kev txhaj tshuaj ntau dua, lossis nrog kev sib xyaw ntawm lwm cov ntshav coagulant Cheebtsam.

Saib xyuas thaum kho

Cov neeg mob hemophilia yuav tsum ua raws li cov lus qhia nram qab no:

• Qoj kev ua si, txhawm rau ntxiv dag zog cov leeg thiab pob qij txha, txhawm rau txhawm los ntshav. Txawm li cas los xij, nws yog ib qho tseem ceeb kom tsis txhob cuam tshuam txog kev sib tw kis las lossis kev ua phem rau lub cev;
• Saib xyuas cov tsos mob ntawm cov tsos mob tshiab, tshwj xeeb hauv menyuam yaus, thiab txo qis nrog kev kho mob;
• Ib txwm muaj tshuaj nyob ze, feem ntau thaum mus ncig ua si;
• Muaj daim ID, raws li ib txoj hlua tes, qhia txog tus kab mob, rau kev kub ntxhov;
• Qhia rau tus mob thaum twg koj ua ib yam twg, xws li kev thov tshuaj tiv thaiv, phais mob hniav lossis txheej txheem kho mob;
• Zam kev noj tshuaj uas pab rau los ntshav, piv txwv li tshuaj aspirin, tshuaj tiv thaiv kev tiv thaiv ntawm lub cev thiab tshuaj tiv thaiv kev puas tsuaj, piv txwv.

Tsis tas li ntawd, kev kho mob lub cev yuav tsum yog ib feem ntawm kev kho cov mob hemophilia, vim nws txhawb kev ua kom lub cev muaj zog, txo qhov kev pheej hmoo ntawm cov teeb meem, xws li mob hemolytic synovitis, uas yog qhov mob ntawm pob qij vim los ntshav, thiab txhim kho cov leeg mob, thiab yog li nws tuaj yeem txo qis qhov kev xav tau noj ntshav txhaws thiab txhim kho lub neej zoo.