Tus Sau: Charles Brown
Hnub Kev Tsim: 2 Lub Ob Hli Ntuj 2021
Hloov Hnub: 24 Lub Rau Hlis Ntuj 2024
Anonim
Maffucci’s syndrome - Animation
Daim Duab: Maffucci’s syndrome - Animation

Zoo Siab

Maffucci syndrome yog ib qho mob uas tsis tshua muaj mob uas cuam tshuam rau cov tawv nqaij thiab pob txha, ua rau cov qog ua pob txha mos, deformities hauv cov pob txha thiab cov tsos mob ntawm cov qog tsaus nti hauv daim tawv nqaij tshwm sim los ntawm kev loj hlob ntawm cov hlab ntsha.

Ntawm ua rau mob Maffucci syndrome lawv yog caj ces thiab cuam tshuam rau txiv neej thiab poj niam sib npaug. Feem ntau, cov tsos mob ntawm tus kabmob pib thaum menyuam yaus nyob ib puag ncig 4-5 xyoos.

LUB Maffucci syndrome tsis muaj kev kho tau, txawm li cas los xij, cov neeg mob tuaj yeem tau txais kev kho mob kom txo cov tsos mob ntawm tus kab mob thiab txhim kho lawv lub neej zoo.

Cov tsos mob ntawm Maffucci Syndrome

Cov tsos mob tseem ceeb ntawm Maffucci syndrome yog:

  • Ob lub qog loj hauv cov pob txha mos ntawm txhais tes, ob txhais ceg thiab cov pob txha ntev ntawm caj npab thiab ceg;
  • Cov pob txha ua rau puas yooj yim thiab tuaj yeem tawg tau yooj yim;
  • Shortening ntawm cov pob txha;
  • Hemangiomas, uas muaj cov pob txha tsaus nti lossis tsaus muag ntawm daim tawv nqaij;
  • Luv;
  • Tsis muaj leeg.

Cov neeg mob Maffucci Syndrome tuaj yeem txhim kho mob pob txha, tshwj xeeb tshaj yog nyob rau pob txha taub hau, tab sis kuj tseem muaj mob ntawm zes qe menyuam lossis mob siab.


O kev kuaj mob ntawm Maffucci syndrome nws yog ua tiav los ntawm kev kuaj lub cev thiab tshuaj ntsuam ntawm cov tsos mob nthuav qhia los ntawm cov neeg mob.

Kev Kho Mob ntawm Maffucci's Syndrome

Kev kho mob ntawm Maffucci's Syndrome suav nrog kev txo qis cov tsos mob ntawm tus kabmob los ntawm kev phais mob kom kho cov pob txha deformities lossis pabcuam ntxiv los pab tus menyuam kev loj hlob.

Cov tib neeg cuam tshuam los ntawm tus kab mob yuav tsum tau sab laj nrog tus kws kho mob orthopedic kom ntsuas cov pob txha pauv, kev loj hlob ntawm pob txha mob thiab kho pob txha lov uas tshwm sim vim tus kab mob. Cov kws kho mob nqaij yuav tsum tau sib tham kom ntsuas qhov pom thiab kev loj hlob ntawm hemangiomas ntawm daim tawv nqaij.

Nws yog ib qho tseem ceeb rau cov neeg mob tau kuaj lub cev ib txwm muaj, duab xoo duab hluav taws xob los yog xoo tomography scans.

Cov duab ntawm Maffucci's Syndrome

Tau qhov twg los:Cov Tsev Tiv Thaiv Kab Mob thiab Tiv Thaiv

Yees Duab 1: Muaj cov qog me me hauv cov pob qij txha ntawm cov ntiv tes yam ntxwv ntawm Maffucci's Syndrome;


Yees Duab 2: Hemangioma ntawm daim tawv nqaij ntawm tus neeg mob nrog Maffucci syndrome.

Pab tau txuas:

  • Hemangioma
  • Tus mob Proteus

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