Hugles-Stovin Cov tsos mob thiab Kev Kho Mob
Zoo Siab
Hugles-stovin syndrome yog ib qho mob uas tsis tshua pom muaj thiab mob hnyav uas ua rau ntau cov hlab ntshav tawm ntawm txoj hlab ntshav txhaws thiab ob peb kis ntawm cov hlab ntsha sib sib zog nqus thaum lub neej. Txij li thawj cov lus piav qhia txog tus kabmob no thoob plaws ntiaj teb, tsawg dua 40 tus neeg tau kuaj pom nyob rau xyoo 2013.
Tus kab mob tuaj yeem nthuav qhia nws tus kheej hauv 3 ntau qib, qhov twg thawj zaug feem ntau nthuav tawm nrog mob thrombophlebitis, theem ob nrog mob leeg ntshav, thiab theem peb thiab theem kawg yog pom los ntawm kev sib tsoo ntawm aneurism uas tuaj yeem ua rau hnoos ntshav thiab tuag.
Tus kws kho mob uas tsim nyog tshaj plaws los txheeb xyuas thiab kho cov mob no yog tus kws kho pob txha thiab txawm hais tias nws qhov teeb meem tseem tsis tau paub meej, nws ntseeg tau tias nws yuav cuam tshuam nrog kev mob vasculitis.
Cov tsos mob
Hugles-stovin cov tsos mob suav nrog:
- Kev hnoos tau ntshav;
- Ua pa nyuaj;
- Hnov txog qhov ua tsis taus pa;
- Mob taub hau;
- Ua npaws kub siab kom hnyav;
- Poob txog kwv yees li 10% ntawm qhov hnyav tsis muaj qhov pom tseeb;
- Papilledema, uas yog kev tso pa tawm ntawm optic papilla uas sawv cev rau kev nce siab hauv lub hlwb;
- O thiab mob hnyav hauv plab hlaub;
- Ob lub zeem muag thiab
- Qhov pom tseeb.
Feem ntau tus neeg mob nrog Hugles-stovin syndrome muaj tsos mob rau ntau lub xyoo thiab tus mob kuj tseem tuaj yeem tsis meej pem nrog Behçet tus kab mob thiab qee cov kws tshawb nrhiav ntseeg tias qhov tsos mob no yog qhov tsis ua tiav ntawm Behçet tus kab mob.
Tus kab mob no tsis tshua pom muaj mob rau menyuam yaus thiab tuaj yeem kuaj tau rau thaum tiav hluas lossis neeg laus tom qab tshaj tawm cov lus qhia dhau los thiab kev kuaj mob xws li kev kuaj ntshav, hauv siab xoo hluav taws xob, MRIs lossis suav tomography ntawm lub taub hau thiab lub hauv siab, ntxiv rau doppler ultrasound los kuaj ntshav thiab lub plawv khiav. Nws tsis muaj qhov kev kuaj mob thiab tus kws kho mob yuav tsum xav tias yog tus mob no vim nws zoo ib yam li Behçet tus kab mob, tab sis tsis muaj nws tus yam ntxwv.
Lub hnub nyoog ntawm cov neeg muaj tus mob no txawv ntawm 12 txog 48 xyoos.
Kev Kho Mob
Cov kev kho mob rau Hugles-Stovin syndrome tsis yog tshwj xeeb heev, tab sis tus kws kho mob yuav pom zoo kom siv cov corticosteroids xws li hydrocortisone lossis prednisone, anticoagulants xws li enoxaparin, kho plawv thiab immunosuppressants xws li Infliximab lossis Adalimumab uas tuaj yeem txo qhov kev pheej hmoo thiab tseem yuav raug rau ntawm aneurysms thiab thrombosis, yog li kev txhim kho lub neej zoo thiab txo qis kev pheej hmoo tuag.
Teeb meem
Hugles-Stovin syndrome tuaj yeem kho tsis yooj yim thiab muaj lub siab tuag vim tias qhov ua rau tus kab mob tsis paub thiab yog li kev kho mob yuav tsis txaus los tswj kev noj qab haus huv ntawm tus neeg cuam tshuam. Raws li muaj qee qhov mob tshwm sim thoob ntiaj teb, cov kws kho mob feem ntau tsis paub txog tus kab mob no, uas tuaj yeem ua rau kev kuaj mob thiab kho mob nyuaj ntxiv.
Tsis tas li ntawd, cov tshuaj tiv thaiv anticoagulants yuav tsum siv nrog kev saib xyuas zoo vim tias qee qhov lawv tuaj yeem ua rau muaj kev pheej hmoo ntxiv los ntshav ntxiv tom qab kev mob pob txha thiab ntshav tau tuaj yeem ua tau zoo heev uas nws tiv thaiv kev saib xyuas lub neej.