Tus Sau: Randy Alexander
Hnub Kev Tsim: 24 Lub Plaub Hlis Ntuj 2021
Hloov Hnub: 1 Lub Xya Hli Ntuj 2024
Anonim
Scleroderma Subtypes (5 Types of Systemic Sclerosis incl. Limited vs Diffuse Scleroderma)
Daim Duab: Scleroderma Subtypes (5 Types of Systemic Sclerosis incl. Limited vs Diffuse Scleroderma)

Zoo Siab

Mauj kab mob Sclerosis (SS)

Systemic sclerosis (SS) yog qhov mob ua haujlwm autoimmune. Qhov no txhais tau tias nws yog qhov xwm txheej ua kom lub cev tiv thaiv kab mob ntawm lub cev. Kev noj qab haus huv cov ntaub so ntswg yog pov tseg vim lub cev tiv thaiv kab mob tsis ncaj ncees lawm nws xav tias nws yog txawv teb chaws cov tshuaj lossis kis mob. Muaj ntau yam haujlwm ua haujlwm autoimmune tuaj yeem cuam tshuam rau lub cev sib txawv.

SS yog qhov txawv txav los ntawm kev hloov hauv cov qauv thiab qhov zoo ntawm daim tawv nqaij. Qhov no yog vim muaj ntau lawm collagen ntau lawm. Collagen yog cov khoom siv ntawm cov ntaub so ntswg sib txuas.

Tab sis qhov kev cuam tshuam no tsis yog muaj feem xyuam rau kev hloov pauv tawv nqaij. Nws tuaj yeem cuam tshuam koj:

  • ntshav hlab
  • cov leeg
  • plawv
  • lub plab zom mov
  • ntsws
  • ob lub raum

Cov yam ntxwv ntawm cov kab mob sclerosis tuaj yeem tshwm sim hauv lwm qhov kev ua haujlwm autoimmune. Thaum qhov no tshwm sim, nws tau hu ua kev sib txuas sib xyaw ua ke.

Tus kab mob no feem ntau pom nyob rau cov neeg 30 txog 50 xyoo, tab sis nws tuaj yeem txheeb xyuas tau txhua lub hnub nyoog. Cov poj niam muaj feem ntau dua li tus txiv neej los soj ntsuam txog tus mob no. Cov tsos mob thiab mob hnyav yog sib txawv ntawm ib tug neeg mus rau lwm tus raws li cov kab ke thiab cov nruab nrog cev.


Kab mob sclerosis no tseem tseem hu ua scleroderma, cov kab mob zuj zus ntawm sclerosis, lossis CREST syndrome. “CREST” sawv cev rau:

  • calcinosis
  • Raynaud's qhov tshwm sim
  • esophageal dysmotility
  • sclerodactyly
  • telangiectasia

CREST syndrome yog ib daim ntawv uas hais tsis sib haum.

Cov duab ntawm System Sclerosis (Scleroderma)

Cov tsos mob ntawm Systemic Sclerosis

SS tsuas yog cuam tshuam rau daim tawv nqaij thaum ntxov ntawm tus kab mob. Koj yuav pom koj daim tawv nqaij tuab thiab thaj chaw uas ncig koj lub qhov ncauj, qhov ntswg, ntiv tes, thiab lwm qhov chaw bony.

Raws li cov xwm txheej mob zuj zus, koj yuav pib ua kom tsis tshua muaj txav ntawm thaj chaw muaj kev puas tsuaj. Lwm cov tsos mob muaj xws li:

  • plaub hau poob
  • calcium tso, los yog qog dawb hauv qab daim tawv nqaij
  • me me, kho cov hlab ntsha hauv qab daim tawv nqaij
  • mob tej pob txha
  • txog siav
  • hnoos qhuav
  • zawv plab
  • cem quav
  • teeb meem nqos
  • esophageal reflux
  • tsam plab mob plab tom qab noj mov

Tej zaum koj yuav pib hnov ​​cov hlab ntshav hauv koj cov ntiv tes thiab ntiv taw. Tom qab ntawv, koj cov lus kawg yuav tig mus ua xim dawb thiab xiav thaum koj nyob hauv qhov txias lossis hnov ​​qhov kev ntxhov siab. Qhov no hu ua Raynaud's qhov xwm txheej.


Cov Teeb Meem ntawm Systemic Sclerosis

SS tshwm sim thaum koj lub cev pib dhau txheej txheem collagen thiab nws ntau ntau hauv koj cov ntaub so ntswg. Collagen yog lub cev cov qauv tseem ceeb uas tsim txhua yam ntawm koj cov ntaub so ntswg.

Cov kws kho mob tsis paub meej tias dab tsi ua rau lub cev ua cov collagen ntau dhau. Vim li cas tiag SS tsis paub.

Kev Pheej Hmoo rau Kab Mob Sclerosis

Cov yam txaus ntshai uas tuaj yeem ua kom koj muaj feem ntau ntawm cov mob no:

  • ua haiv neeg Khab
  • ua neeg Asmeskas-Asmeskas
  • ua poj niam
  • siv cov tshuaj khomob xws li Bleomycin
  • raug rau silica hmoov av thiab cov kuab tshuaj organic

Nws tsis muaj txoj hauv kev los tiv thaiv lwm tus SS dua li los txo cov kev pheej hmoo uas koj tuaj yeem tswj hwm.

Kev kuaj mob ntawm System Sclerosis

Thaum kuaj mob lub cev, koj tus kws kho mob tuaj yeem txheeb xyuas cov kev hloov tawv nqaij uas muaj tsos mob ntawm SS.

Mob ntshav siab tuaj yeem tshwm sim los ntawm lub raum hloov pauv ntawm sclerosis. Koj tus kws kho mob yuav xaj kuaj ntshav zoo li kuaj ntshav, mob rheumatoid factor, thiab feem ntshav poob.


Lwm yam kev kuaj mob tuaj yeem suav nrog:

  • lub hauv siab X-ray
  • ib tug mob txeeb zig
  • CT scan ntawm lub ntsws
  • muab nqaij los kuaj

Kev Kho Mob rau Kab Mob Sclerosis

Kev kho mob tsis tuaj yeem kho tus mob, tab sis nws tuaj yeem pab txo cov tsos mob thiab qeeb qeeb mob. Txoj kev kho yog ib txwm nyob ntawm tus neeg mob thiab yuav tsum tiv thaiv kom txhob mob ntxiv.

Kev kho rau cov tsos mob dav dav tuaj yeem suav nrog:

  • corticosteroids
  • cov tshuaj tiv thaiv kab mob, xws li methotrexate lossis Cytoxan
  • nonsteroidal tshuaj tiv thaiv

Nyob ntawm koj cov tsos mob, kev kho kuj tuaj yeem suav nrog:

  • tshuaj noj ntshav siab
  • tshuaj kho mob rau kev ua pa
  • kev pab kho lub cev
  • kev kho lub teeb, xws li ultraviolet A1 phototherapy
  • nitroglycerin tshuaj pleev los kho thaj chaw thaj chaw ntawm kev nruj ntawm daim tawv nqaij

Koj tuaj yeem hloov pauv kev ua neej nyob kom muaj kev noj qab haus huv nrog scleroderma, xws li zam kev haus luam yeeb, ua kom lub cev txav mus deb, thiab zam tej zaub mov uas ua rau kub siab.

Muaj teeb meem tshwm sim ntawm System Sclerosis

Qee cov neeg nrog SS muaj kev loj hlob ntawm lawv cov tsos mob. Teeb meem tuaj yeem suav nrog:

  • lub plawv tsis ua hauj lwm
  • mob cancer
  • raum tsis ua hauj lwm
  • ntshav siab

Qhov Kev Pom Zoo rau Cov Neeg Muaj Kab Mob Sclerosis Yog Dab Tsi?

Cov kev kho rau SS tau ruaj khov nyob rau hauv 30 xyoo dhau los. Txawm hais tias tseem tsis tau muaj kev kho tus mob SS los, nws muaj ntau yam kev kho uas tuaj yeem pab koj tswj hwm koj tus mob. Tham nrog koj tus kws kho mob yog tias muaj qee yam ntawm koj cov tsos mob tau nyob hauv txoj kev ntawm koj lub neej txhua hnub. Lawv tuaj yeem ua haujlwm nrog koj los kho koj txoj kev npaj khomob.

Koj kuj yuav tsum nug koj tus kws kho mob los pab koj nrhiav cov pab txhawb hauv ib cheeb tsam rau SS. Tham nrog lwm tus neeg uas muaj kev paub zoo ib yam li koj tuaj yeem ua kom yooj yim dua tiv nrog mob ntsig txog mob.

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