Txhua Yam Koj Yuav Tsum Tau Paub Txog Porphyria Cutanea Tarda

Zoo Siab

• Cov tsos mob
• Cov duab ntawm porphyria cutanea tarda
• Ua rau
• Yam pheej hmoo
• Qhov tshwm sim
• Kev kuaj mob
• Kev Kho Mob
• Outlook

Txheej txheem cej luam

Porphyria cutanea tarda (PCT) yog ib hom kev muaj ntshav lossis tawv ntshav uas cuam tshuam rau daim tawv nqaij. PCT yog ib qho ntawm kev sib txawv ntawm feem ntau ntawm porphyria. Qee lub sijhawm nws raug xa mus rau kis raws li vampire kab mob. Ntawd yog vim cov neeg muaj tus mob no feem ntau hnov ​​cov tsos mob tom qab raug tshav ntuj.

Cov tsos mob

Feem ntau ntawm cov tsos mob ntawm porphyria cutanea tarda tshwm nyob rau ntawm daim tawv nqaij. Cov tsos mob tshwm sim suav nrog:

• cov hlwv ntawm daim tawv uas raug tshav, suav nrog txhais tes, ntsej muag, thiab caj npab
• photosensitivity, uas txhais tau tias koj daim tawv yog lub hnub
• nyias lossis tawv nqaij tawv
• nce cov plaub hau kev loj hlob, feem ntau ntawm ntsej muag
• ua kaub puab thiab caws pliav
• liab, o, lossis khaus ntawm daim tawv nqaij
• qhov ncauj tawm tom qab raug mob me rau ntawm daim tawv nqaij
• hyperpigmentation, uas txhais tau hais tias thaj ua rau thaj tawv nqaij tsaus dua
• tso zis uas tsaus dua li ib txwm los yog xim av
• mob siab puas tsuaj

Tom qab cov hlwv ua rau koj daim tawv, tawv nqaij yuav tev tawv. Nws yog ib qho kuj yuav ua rau muaj caws pliav tshwm thaum cov hlwv zoo tuaj.

Hyperpigmentation patches feem ntau tshwm sim rau ntawm lub ntsej muag, tes, thiab caj dab.

Cov duab ntawm porphyria cutanea tarda

Ua rau

Porphyria cutanea tarda tuaj yeem tshwm sim los ntawm ntau yam. Cov ua yog feem ntau muab cais raws li caj los sis kis tau.

Cov caj ces uas nquag pom muaj xws li:

• tsev neeg keeb kwm ntawm porphyria cutanea tarda
• pub yug los muaj lub siab ua rau daim siab enzyme uroporphyrinogen decarboxylase
• tsev neeg muaj keeb kwm muaj kab mob siab lossis mob cancer
• ntau lub siab hlau dua li ib txwm

Feem ntau nrhiav tau muaj xws li:

• haus cawv
• siv tshuaj kho estrogen
• siv tshuaj tiv thaiv qhov ncauj
• raug rau qee yam ib puag ncig lossis tshuaj kuab, xws li Agent Txiv Kab Ntxwv
• noj ntau dhau hlau
• haus luam yeeb
• muaj mob rau daim siab C
• muaj HIV

Qee qhov xwm txheej, nws tsis tuaj yeem txiav txim siab ua kom muaj kab mob porphyria cutanea tarda.

Yam pheej hmoo

Koj yuav muaj feem ntau dua ntawm kev coj pob txha npau yog tias koj haus luam yeeb lossis haus cawv. Koj tseem yuav muaj tus mob no ntau yog tias koj muaj kab mob siab C lossis HIV.

Raug rau qee yam tshuaj lom neeg, xws li Agent Orange, tuaj yeem ua koj qhov phom sij ntau ntxiv. Koj tuaj yeem raug cov tshuaj no yog tias koj yog ib tus qub tub rog uas ua haujlwm hauv thaj chaw uas muaj Agent Orange.

Qhov tshwm sim

Porphyria cutanea tarda tuaj yeem cuam tshuam rau txiv neej thiab poj niam. Nws feem ntau pom tshwm tom qab hnub nyoog 30, yog li ntawd nws tsis tshua pom muaj nyob hauv menyuam yaus lossis tub ntxhais hluas.

Porphyria cutanea tarda cuam tshuam rau tib neeg thoob ntiaj teb thiab tsis txwv rau cheeb tsam lossis lub tebchaws tshwj xeeb. Nws tau kwv yees tias 1 ntawm 10,000 txog 25,000 tus neeg muaj tus mob no.

Kev kuaj mob

Koj tus kws kho mob yuav kuaj lub cev, kuaj cov tsos mob, thiab sau koj li keeb kwm kho mob. Ib qho ntxiv, lawv yuav siv cov ntawv hauv qab no los kuaj mob porphyria cutanea tarda:

• kuaj ntshav
• kuaj zis
• kuaj cov quav
• muab nqaij los kuaj

Tus kws kho mob yuav kuaj xyuas koj cov qib ntawm porphyrin thiab daim siab ua haujlwm siab. Kev kuaj keeb kwm tuaj yeem pom zoo rau cov neeg uas muaj keeb kwm tsev neeg ntawm tus mob no.

Kev Kho Mob

Cov kev kho mob rau kab mob porphyria cutanea tarda tsom rau kev tswj hwm thiab nres cov tsos mob. Kev ua neej hloov, xws li txwv kev haus cawv ntau thiab tsis haus luam yeeb, kuj yuav pab tau.

Cov kev xaiv ntau hom muaj xws li:

• phlebotomy, uas yog kev tshem tawm ntshav kom txo cov hlau
• chloroquine (Aralen)
• hydroxychloroquine (Plaquenil)
• tshuaj kho mob
• hlau chelators
• kho cov kab mob uas ua rau mob rau cov leeg (porphyria cutanea tarda), xws li HCV lossis HIV

Phlebotomy yog ib qho kev kho mob feem ntau rau cov kab mob porphyria cutanea tarda. Cov tshuaj antimalarial kuj tseem siv.

Hloov pauv ntawm txoj kev ua neej los kho porphyria cutanea tarda suav nrog:

• zam kev haus cawv
• tsis haus luam yeeb
• zam kev tshav ntuj
• siv tshuaj pleev thaiv hnub
• zam kev raug mob rau daim tawv nqaij
• tsis txhob noj tshuaj estrogens

Tej zaum koj yuav tsum hnav hnub ci, tsho ntev, thiab lub kaus mom kom zam dhau lub hnub.

Porphyria cutanea tarda tuaj yeem ua rau muaj kev pheej hmoo mob qog nqaij hlav lossis mob pob txha, uas yog ua kom nqaij hlav. Vim li no thiaj li tseem ceeb uas tsis txhob haus cawv yog tias koj muaj tus mob no.

Outlook

Porphyria cutanea tarda feem ntau cuam tshuam rau cov neeg laus uas laus dua 30. Nws yog cov ntshav uas feem ntau cuam tshuam rau daim tawv nqaij. Koj cov tawv nqaij yuav nkag siab ntau dua rau lub hnub, yog li koj yuav tau siv kev ceeb toom ntau ntxiv kom zam dhau lub hnub. Cov hlwv yuav muaj los ntawm tus mob no.

Koj tus kws kho mob yuav pom zoo kom kho cov kab mob sib txawv rau cov kab mob nqaij pob txha. Cov tshuaj Phlebotomy thiab cov tshuaj antimalarial yog qhov kev xaiv ntau hom kev kho mob.

Yog tias koj tab tom nrhiav kev txhawb nqa, tshawb xyuas cov npe txheeb xyuas ntawm qhov zoo tshaj ntawm cov tawv nqaij mob hlwb ntawm lub xyoo.