Kab mob pob txha caj qaum: ua rau, cov tsos mob thiab kev kho mob

Zoo Siab

• Dab tsi ua rau muaj mob spherocytosis
• Cov tsos mob tseem ceeb
• Yuav kho tus mob li cas

Hereditary spherocytosis yog ib hom kab mob caj ces ua cim los ntawm kev hloov pauv ntawm cov qe ntshav liab, uas txaus siab rau nws qhov kev rhuav tshem, thiab yog vim li ntawd thiaj suav tias yog tus mob ntshav khov (hemolytic anemia). Kev hloov pauv ntawm daim nyias nyias ntawm cov qe ntshav liab ua rau lawv me thiab tsis tuaj yeem tiv taus ntau dua li ib txwm, tau yooj yim los ntawm tus po.

Spherocytosis yog ib hom kab mob muaj keeb, uas koom nrog tus neeg txij thaum yug los, txawm li cas los xij, nws tuaj yeem hloov kho nrog kev mob ntshav tsis txaus ntawm qhov ua tsis zoo. Yog li, qee kis muaj qee zaum tsis muaj tsos mob thiab nyob rau lwm tus, pallor, nkees nkees, daj ntseg, ua kom tus txha caj qaum thiab hloov kev loj hlob, piv txwv li, tuaj yeem pom.

Txawm hais tias tsis muaj kev kho tau tus mob, spherocytosis muaj kev kho mob, uas yuav tsum tau coj los ntawm hematologist, thiab kev hloov cov tshuaj folic acid kuj yuav qhia tau thiab, feem ntau qhov hnyav, tshem tawm tus po, uas yog hu ua splenectomy, thiaj li tswj tau tus mob Cov.

Dab tsi ua rau muaj mob spherocytosis

Tus kab mob heheter spherocytosis tshwm sim los ntawm kev hloov caj ces uas ua rau muaj kev pauv ntau ntau los sis zoo ntawm cov protein ua rau daim nyias nyias ntawm cov ntshav liab, uas nrov npe hu ua ntshav liab. Cov kev hloov pauv ntawm cov protein no ua rau poob ntawm kev ua kom nruj thiab tiv thaiv kab mob ntshav liab, uas ua rau lawv puas yooj yim dua thiab ntawm qhov loj me me, txawm hais tias cov ntsiab lus zoo ib yam, tsim cov qe ntshav me, nrog cov sib npaug thiab ntau xim.

Kev mob ntshav khov tshwm sim vim hais tias spherocytes, vim cov ntshav liab ua rau hauv spherocytosis hu ua, feem ntau raug pov tseg hauv tus txha caj qaum, tshwj xeeb tshaj yog thaum hloov pauv tseem ceeb thiab muaj qhov tsis taus thiab tsis taus los ntawm microcirculation ntawm cov ntshav los ntawm cov khoom no.

Cov tsos mob tseem ceeb

Spherocytosis tuaj yeem muab cais ua qhov sib xyaw me, nruab nrab lossis mob hnyav. Yog li, cov neeg mob spherocytosis me me yuav tsis muaj cov tsos mob, thaum cov neeg uas muaj tus mob spherocytosis me me mus rau mob hnyav yuav muaj qhov sib txawv ntawm cov cim thiab cov tsos mob xws li:

• Cov ntshav tsis tu ncua;
• Pallor;
• Nkees nkees thiab thev tsis txaus rau kev tawm dag zog lub cev;
• Nce bilirubin hauv cov ntshav thiab daj, uas yog qhov xim daj ntawm daim tawv nqaij thiab cov leeg nqaij;
• Tsim cov pob zeb bilirubin hauv lub zais khoom;
• Ntxiv spleen loj.

Txhawm rau kuaj mob raws keeb kwm spherocytosis, ntxiv rau kev soj ntsuam hauv chaw kho mob, hematologist tuaj yeem xaj kuaj ntshav xws li suav cov ntshav, reticulocyte suav, ntsuas bilirubin thiab peripheral ntshav smear uas qhia kev hloov pauv ntawm cov ntshav tsis zoo.Kev tshuaj ntsuam xyuas rau osmotic fragility kuj qhia, uas ntsuas qhov tsis kam ntawm kev tua cov qe ntshav liab.

Yuav kho tus mob li cas

Tus kab mob pob txha caj dab tsis muaj tshuaj kho tau, txawm li cas los xij, hematologist tuaj yeem pom zoo cov kev kho mob uas tuaj yeem txo cov kev mob phem zuj zus thiab cov tsos mob, raws li tus neeg mob xav tau. Hauv cov tib neeg uas tsis pom tsos mob ntawm tus kab mob, tsis tas yuav muaj kev kho mob tshwj xeeb.

Kev hloov pauv ntawm cov folic acid yog qhov pom zoo vim, vim tias muaj ntau cov qog ua cov ntshav liab, cov khoom siv no yog qhov tsim nyog ntxiv rau kev tsim cov hlwb tshiab hauv hlwb pob txha.

Cov kev kho mob tseem ceeb yog tshem cov hnoos qeev los ntawm kev phais mob, uas feem ntau tau qhia rau cov menyuam yaus hnub nyoog 5 lossis 6 xyoo uas muaj mob ntshav tsis txaus, xws li cov neeg uas muaj hemoglobin qis dua 8 mg / dl hauv cov ntshav suav, los yog qis dua 10 mg / dl yog tias muaj cov tsos mob tseem ceeb lossis teeb meem xws li mob lub raum zais zis. Kev phais mob tuaj yeem ua tiav rau cov menyuam yaus uas muaj kev loj hlob qeeb vim tus kabmob.

Cov tib neeg uas raug rho tawm qhov hnoos qeev feem ntau yuav muaj qee yam kev kis mob lossis mob thromboses, yog li txhaj tshuaj tiv thaiv, xws li mob ntsws, yog xav tau, ntxiv rau kev siv tshuaj ASA los tswj ntshav txhaws. Tshawb xyuas seb qhov phais mob rau kev tshem tawm tus po thiab ua li cas thiaj li kho mob tas.