Phenylketonuria Khoom Noj: Tso Cai, Txwv tsis pub cov zaub mov thiab ntawv qhia zaub mov

Zoo Siab

• Cov khoom noj pub rau hauv phenylketonuria
• Cov zaub mov raug txwv hauv phenylketonuria
• Qhov ntau ntawm phenylalanine tso cai los ntawm lub hnub nyoog
• Qauv ntawv qhia zaub mov
• Piv xam cov ntawv qhia zaub mov rau ib tus menyuam muaj 3 xyoos nrog phenylketonuria:

Hauv kev noj haus rau cov neeg muaj phenylketonuria nws yog qhov tseem ceeb heev los tswj kev noj cov phenylalanine, uas yog cov amino acids uas muaj feem ntau hauv cov zaub mov muaj protein ntau, xws li nqaij, ntses, qe, mis thiab cov khoom noj siv mis. Yog li, cov neeg uas muaj phenylketonuria yuav tsum tau kuaj ntshav tas li kom ntsuas cov phenylalanine hauv cov ntshav thiab, ua ke nrog kws kho mob, suav cov phenylalanine ntau uas lawv tuaj yeem noj thaum nruab hnub.

Txij li nws yog qhov yuav tsum tau zam ntawm cov khoom noj uas muaj protein ntau, phenylketonurics kuj tseem yuav tsum siv cov khoom noj muaj protein tsis muaj phenylalanine, vim tias cov protein muaj cov zaub mov tseem ceeb hauv lub cev, uas tsis tuaj yeem raug tshem tawm tag nrho.

Tsis tas li ntawd, thaum tsis muaj phenylalanine ntau ntxiv, lub cev xav tau ntau dua ntawm cov tshuaj tyrosine ntau dua, uas yog lwm cov amino acid uas yuav los ua qhov tseem ceeb rau kev loj hlob thaum tsis muaj phenylalanine. Vim li no, feem ntau nws yuav tsum tau ntxiv nrog tyrosine ntxiv rau kev noj haus. Tshawb xyuas tias lwm cov kev ceev faj yog qhov tseem ceeb hauv kev kho phenylketonuria.

Cov khoom noj pub rau hauv phenylketonuria

Cov zaub mov uas pub rau cov neeg muaj phenylketonuria yog:

• Txiv Hmab Txiv Ntoo:kua, pear, melon, txiv quav ntswv nyoos, acerola, txiv qaub, jabuticaba, currant;
• Ib txhia hmoov nplej: hmoov txhuv nplej siab, qos ntoo;
• Khaub noom: qab zib, txiv hmab txiv ntoo jellies, zib ntab, sago, cremogema;
• Cov rog: zaub roj, zaub cream tsis muaj mis nyuj thiab kev ua haujlwm dhau los;
• Lwm tus: tswm ciab, lollipops, dej qab zib, kua txiv hmab txiv ntoo tsis muaj mis nyuj, kas fes, teas, zaub gelatin ua nrog cov seaweed, mustard, kua txob.

Tseem muaj lwm yam zaub mov uas raug tso cai rau phenylketonurics, tab sis qhov ntawd yuav tsum raug tswj. Cov zaub mov no yog:

• Cov zaub nyob rau hauv dav dav, xws li spinach, chard, lws suav, taub dag, yams, qos yaj ywm, qos yaj ywm qab zib, okra, beets, zaub paj, carrots, chayote.
• Lwm tus: cov nplej tsis muaj qe, mov, txiv maj phaub dej.

Tsis tas li ntawd, muaj cov qauv tshwj xeeb ntawm cov khoom xyaw nrog tsawg dua ntawm phenylalanine, xws li mov, nplej hmoov nplej lossis nplej zom, piv txwv.

Txawm hais tias kev txwv kev noj zaub mov zoo rau phenylketonurics, muaj ntau yam kev lag luam uas tsis muaj phenylalanine hauv lawv cov lus sib xyaw lossis qhov tsis zoo hauv cov amino acid no. Txawm li cas los xij, txhua yam nws tseem ceeb heev uas yuav tsum tau nyeem ntawm cov khoom ntim yog tias nws muaj phenylalanine.

Saib cov npe ua tiav rau cov khoom noj uas raug tsocai thiab muaj ntau npaum li cas ntawm phenylalanine.

Cov zaub mov raug txwv hauv phenylketonuria

Cov zaub mov raug txwv hauv phenylketonuria yog cov nplua nuj nyob hauv phenylalanine, uas yog cov zaub mov muaj protein ntau, xws li:

• Tsiaj cov khoom noj: nqaij, ntses, nqaij nruab deg, mis thiab nqaij nqaij, qe, thiab cov khoom lag luam xws li cov hnyuv ntxwm, hnyuv ntxwm, nqaij npuas kib, nqaij npua.
• Cov khoom noj ntawm tsob ntoo keeb kwm: cov nplej, txhuv, taum pauv, taum pauv, taum pauv, taum pauv thiab taum pauv, txiv ntseej, txiv ntoo, txiv laum huab xeeb, hazelnuts, almonds, pistachios, txiv ntoo thuv;
• Cov khoom qab zib nrog aspartame lossis cov khoom noj uas muaj cov qab zib no;
• Cov khoom uas muaj cov khoom noj uas raug txwv, xws li ncuav mog qab zib, ncuav qab zib thiab ncuav.

Raws li kev noj haus ntawm phenylketonurics tsis muaj protein ntau, cov neeg no yuav tsum noj cov tshuaj tshwj xeeb ntawm cov amino acids uas tsis muaj phenylalanine txhawm rau kom paub tseeb tias kev loj hlob zoo thiab ua haujlwm ntawm lub cev.

Qhov ntau ntawm phenylalanine tso cai los ntawm lub hnub nyoog

Tus nqi ntawm phenylalanine uas tuaj yeem noj txhua hnub nws txawv raws lub hnub nyoog thiab qhov hnyav, thiab kev pub mis ntawm phenylketonurics yuav tsum tau ua nyob rau hauv ib txoj kev uas tsis pub dhau qhov tso cai phenylalanine qhov tseem ceeb. Cov npe hauv qab no qhia cov txiaj ntsig tau tso cai ntawm no amino acid raws li pawg hnub nyoog:

• Nruab nrab ntawm 0 txog 6 hli: 20 txog 70 mg / kg ib hnub;
• Nruab nrab ntawm 7 hlis txog 1 xyoos: 15 txog 50 mg / kg ib hnub;
• Los ntawm 1 txog 4 xyoos ntawm lub hnub nyoog: 15 txog 40 mg / kg ib hnub;
• Los ntawm 4 rau 7 xyoo ntawm lub hnub nyoog: 15 txog 35 mg / kg ib hnub;
• Txij 7 pib: 15 txog 30 mg / kg ib hnub.

Yog tias tus neeg muaj phenylketonuria noj cov phenylalanine tsuas yog nyob hauv cov nyiaj uas tau tso cai, lawv txoj kev tsav thiab kev txhim kho yuav tsis muaj kev cuam tshuam. Txhawm rau paub ntau ntxiv saib: Nkag siab zoo dua Phenylketonuria yog dab tsi thiab kho nws li cas.

Qauv ntawv qhia zaub mov

Cov ntawv qhia zaub mov ntawm cov khoom noj rau phenylketonuria yuav tsum yog tus kheej thiab npaj los ntawm tus kws qhia zaub mov noj haus, vim nws yuav tsum coj mus rau hauv tus neeg lub hnub nyoog, ntau npaum li cas phenylalanine pub thiab cov txiaj ntsig ntawm kev kuaj ntshav.

Piv xam cov ntawv qhia zaub mov rau ib tus menyuam muaj 3 xyoos nrog phenylketonuria:

Kev tiv taus: 300 mg phenylalanine ib hnub

Nws kuj tseem ceeb tias tus neeg thiab lawv tsev neeg yuav tsum xyuas cov ntawv cim khoom seb puas muaj cov khoom noj muaj phenylalanine thiab nws cov ntsiab lus yog dab tsi, yog li kho cov khoom noj uas tuaj yeem noj tau.