Dab tsi yog Alport's disease, cov tsos mob thiab yuav kho li cas

Zoo Siab

• Cov tsos mob tseem ceeb
• Dab tsi ua rau tus mob
• Yuav ua li cas kom paub meej tias kuaj mob
• Yuav kho tus mob li cas

Alport syndrome yog ib qho kev mob tshwm sim tsawg heev uas ua rau muaj kev puas tsuaj me me rau cov hlab ntshav me me uas nyob hauv lub raum glomeruli ntawm lub raum, tiv thaiv lub cev kom tsis tuaj yeem lim ntshav tau cov ntshav thiab ua rau pom cov tsos mob xws li ntshav hauv cov zis thiab nce protein ntau ntxiv hauv kev sim ntshav.

Ntxiv rau qhov cuam tshuam rau lub raum, cov tsos mob no tseem tuaj yeem tsim teeb meem hauv kev hnov ​​lus lossis pom, vim nws txwv tsis pub cov khoom noj protein uas tseem ceeb rau kev ua haujlwm ntawm lub qhov muag thiab pob ntseg.

Alport's syndrome tsis muaj kev kho tau, tab sis kev kho mob pab txo cov tsos mob thiab tseem ncua kev tiv thaiv tus kab mob, tiv thaiv lub raum kev ua haujlwm.

Cov tsos mob tseem ceeb

Cov tsos mob tshwm sim feem ntau ntawm Alport's syndrome muaj xws li:

• Cov ntshav hauv cov zis;
• Ntshav siab;
• O ntawm cov ceg, pob taws, taw thiab lub ntsej muag.

Tsis tas li ntawd, tseem muaj cov rooj lus uas hnov ​​thiab pom kev zoo cuam tshuam los ntawm tus kabmob, ua rau muaj kev nyuaj rau hnov ​​thiab pom.

Yog tias tsis ceev faj, cov kab mob yuav tuaj yeem mob raum tsis ua haujlwm ntev thiab yuav tsum tau lim ntshav lossis hloov raum.

Dab tsi ua rau tus mob

Alport's syndrome tshwm sim los ntawm kev hloov pauv ntawm cov caj ces uas muaj cov lus qhia rau kev tsim cov protein hu ua hom IV collagen. Hom collagen no yog ib feem ntawm lub raum lub ntsej muag glomeruli thiab, yog li ntawd, thaum nws tsis nyob, cov hlab ntshav hauv cov cheeb tsam no tau txais kev raug mob thiab kho mob, ua rau lub raum tsis ua haujlwm.

Zoo li no, tus collagen no tseem muaj nyob rau hauv pob ntseg thiab qhov muag thiab, yog li ntawd, cov kev hloov hauv cov kabmob no kuj tseem tuaj yeem dhau sijhawm.

Yuav ua li cas kom paub meej tias kuaj mob

Tsis muaj kev kuaj tshwj xeeb rau kev kuaj mob Alport's syndrome, yog li koj tus kws kho mob yuav xaj kuaj ntau yam, xws li ntsuas zis, kuaj ntshav lossis kuaj lub raum kom paub tias puas muaj dab tsi hloov uas yuav ua rau tus mob.

Yuav kho tus mob li cas

Kev kho mob rau Alport's syndrome tau ua nrog lub hom phiaj ntawm kev mob tshwm sim, vim tias tsis muaj daim ntawv tshwj xeeb los kho. Yog li, nws yog qhov siv heev rau kev siv tshuaj kho mob ntshav siab thiab tshuaj diuretics, txhawm rau tswj ntshav siab thiab tiv thaiv kev mob ntshav ntawm lub raum.

Tsis tas li ntawd, nws tseem pom zoo kom tswj cov zaub mov muaj ntsev kom tiv thaiv lub raum ua haujlwm ntau. Ntawm no yog yuav ua li cas thiaj tuav tau kev noj haus ntawm hom no.

Feem ntau, uas lub raum cuam tshuam ntau heev thiab tsis muaj kev txhim kho hauv cov tsos mob, nws yuav tsim nyog pib lim ntshav los yog muaj lub raum hloov ntshav.