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Hnub Kev Tsim: 26 Lub Ib Hli Ntuj 2021
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Txhua Hais Txog Antiphospholipid Syndrome (Hughes Syndrome) - Noj Qab Haus Huv
Txhua Hais Txog Antiphospholipid Syndrome (Hughes Syndrome) - Noj Qab Haus Huv

Zoo Siab

Txheej txheem cej luam

Hughes syndrome, tseem hu ua "nplaum ntshav syndrome" los yog antiphospholipid syndrome (APS), yog ib tus mob autoimmune uas cuam tshuam txoj kev uas koj cov ntshav khi ua ke, lossis txhaws. Hughes syndrome yog suav tias yog tsawg.

Cov poj niam uas tau rov muaj dua me nyuam thiab cov neeg uas muaj mob hlab ntsha tawg ua ntej hnub nyoog 50 qee zaum pom tau tias Hughes syndrome yog qhov pib. Nws tau kwv yees tias Hughes mob yuav cuam tshuam peb mus rau tsib zaug ntau tus poj niam li txiv neej.

Txawm hais tias qhov ua rau Hughes syndrome tsis paub meej, cov neeg tshawb nrhiav ntseeg hais tias kev noj zaub mov noj, kev ua neej, thiab caj ces ntawm txhua tus muaj feem cuam tshuam txog kev tsim tus mob.

Cov tsos mob ntawm Hughes syndrome

Cov tsos mob ntawm tus mob Hughes yog qhov nyuaj rau pom, vim tias cov ntshav txhaws tsis yog yam uas koj tuaj yeem yooj yim txheeb xyuas yam tsis muaj lwm yam mob lossis lwm yam kev mob. Qee zaum Hughes syndrome ua rau lub ntsej muag liab tawm los ntshav los ntawm koj lub qhov ntswg thiab cov pos hniav.

Lwm yam cim uas koj yuav muaj Hughes syndrome suav nrog:

  • rov muaj dua nchuav lossis menyuam poob los
  • ntshav txhaws nyob hauv koj ob txhais ceg
  • transient ischemic nres (TIA) (zoo ib yam li mob hlab ntsha tawg, tab sis tsis muaj cov leeg hlab ntshav mus tas li)
  • mob stroke, tshwj xeeb yog koj hnub nyoog qis dua 50 xyoos
  • cov ntshav platelet tsawg
  • plawv nres

Cov neeg uas mob lupus yuav muaj mob ntsws Hughes.


Muaj qee zaus, yog tsis kho tus mob Hughes syndrome tuaj yeem nce ntxiv yog tias koj muaj kab mob ntshav txhaws ua ke thoob plaws lub cev. Qhov no hu ua catastrophic antiphospholipid syndrome, thiab nws tuaj yeem ua kev puas tsuaj rau koj cov nruab nrog cev thiab tuag taus.

Cov Ua rau Hughes syndrome

Cov kws tshawb nrhiav tseem ua haujlwm kom nkag siab txog cov laj thawj ntawm Hughes syndrome. Tab sis lawv tau txiav txim siab tias muaj caj ces ntawm kev ua si.

Hughes mob yuav tsis kis ncaj qha los ntawm niam txiv, txoj kev uas lwm yam kev mob hauv ntshav, zoo li hemophilia, tuaj yeem yog. Tab sis kev muaj ib tug hauv tsev neeg nrog Hughes syndrome txhais tau tias koj haj yam muaj tus mob no.

Nws muaj peev xwm hais tias ib lub noob txuas nrog rau lwm yam kev ua phom sij kuj ua rau Hughes syndrome. Qhov ntawd yuav piav qhia tias vim li cas cov tib neeg muaj tus mob no feem ntau muaj lwm yam teeb meem autoimmune.

Muaj qee yam voos lossis kab mob kis tau, nyiam E. coli lossis cov kab mob parvovirus, tuaj yeem ua rau Hughes syndrome tuaj yeem tsim kho tom qab tau kis tus kabmob. Cov tshuaj los tswj tus mob vwm, nrog rau qhov ncauj kom txhob muaj me nyuam, kuj tseem yog lub luag hauj lwm ua rau tus mob.


Cov xwm txheej ib puag ncig zoo li no kuj tseem yuav cuam tshuam nrog kev ua lub neej - zoo li tsis tau ua kom tawm dag zog txaus thiab noj zaub mov kom muaj roj cholesterol siab - thiab ua rau Hughes syndrome.

Tab sis cov menyuam yaus thiab cov neeg laus uas tsis muaj ib yam kabmob li no, yam tseem ceeb rau lub neej, lossis kev siv tshuaj noj tseem tuaj yeem tau txais tus mob Hughes txhua lub sijhawm.

Yuav muaj ntau cov kev tshawb fawb ntxiv los txheeb cov teeb meem ntawm Hughes syndrome.

Kev kuaj mob ntawm tus mob Hughes

Hughes syndrome tau kuaj pom los ntawm kev sim ntshav ntau zaus. Cov kev kuaj ntshav no ntsuam xyuas cov tshuaj tiv thaiv uas koj lub cev tiv thaiv kab mob ua rau pom seb lawv coj tus cwj pwm li cas lossis yog tias lawv tsom lwm lub hlwb noj qab haus huv.

Ib qho kev kuaj ntshav sib xws uas txheeb xyuas tus mob Hughes yog hu ua kev siv tshuaj tiv thaiv kab mob. Koj yuav tsum tau muaj ob peb txoj kev ua no los txiav txim tawm lwm yam mob.

Hughes syndrome tuaj yeem ua tsis ncaj ncees raws li ntau tus mob sclerosis vim tias ob qhov xwm txheej muaj cov tsos mob zoo ib yam. Kev tshuaj xyuas kom zoo yuav tsum txiav txim siab koj tus mob raug, tab sis nws tuaj yeem siv qee lub sijhawm.


Kev kho mob ntawm Hughes syndrome

Hughes syndrome tuaj yeem kho kho ntshav txhaws (cov tshuaj uas ua rau koj txo cov ntshav txhaws).

Qee cov neeg uas muaj tus mob Hughes tsis hais qhia txog cov ntshav txhaws thiab yuav tsis tas yuav tau txais kev kho mob tshaj li cov tshuaj aspirin txhawm rau tiv thaiv kev pheej hmoo ntawm txhaws.

Cov tshuaj tiv thaiv Anticoagulant, xws li warfarin (Coumadin) kuj yuav raug muab tshuaj, tshwj xeeb yog tias koj muaj keeb kwm mob ntsws txoj hlab ntsws loj.

Yog koj tseem tabtom sim cev xeeb tub kom txog rau lub sijhawm thiab muaj tus mob Hughes, koj yuav tau noj tshuaj aspirin tsawg los yog noj ib hnub ib zaug ntshav heparin.

Cov poj niam uas muaj tus mob Hughes yog 80 feem pua ​​uas yuav coj tus me nyuam mus rau ib lub sijhawm yog lawv raug kuaj thiab pib txoj kev kho mob yooj yim.

Kev noj haus thiab kev tawm dag zog rau Hughes syndrome

Yog tias koj raug kuaj pom tias muaj Hughes syndrome, noj zaub mov kom zoo tuaj yeem txo qhov kev pheej hmoo ntawm cov teeb meem tshwm sim, zoo li mob stroke.

Noj zaubmov uas muaj txiv ntoo thiab zaub ntau ntau thiab cov uas muaj rog thiab muaj suab thaj ntau yuav ua rau koj lub plawv khiav lag luam zoo dua, ua rau cov ntshav txhaws.

Yog tias koj tab tom kho Hughes syndrome nrog warfarin (Coumadin), Mayo Clinic qhia koj kom paub meej tias koj yuav noj haus vitamin K ntau npaum li cas.

Txawm hais tias muaj cov vitamin K me me yuav tsis muaj feem cuam tshuam rau koj txoj kev kho mob, kev hloov pauv ntawm koj li kev noj tshuaj vitamin K tuaj yeem ua rau koj cov tshuaj noj tau hloov pauv ntau. Zaub cob pob, Zaub pob txawv, taum garbanzo, thiab avocado yog qee cov zaub mov uas muaj vitamin K ntau.

Kev tawm dag zog kom ib ce tawm hws tuaj yeem yog ib feem ntawm kev tswj koj tus mob. Zam kev haus luam yeeb thiab tswj lub cev kom zoo rau koj lub cev kom ua rau koj lub plawv thiab cov leeg muaj zog thiab muaj ntau yam ntxiv tiv thaiv kev puas tsuaj.

Qhov kev xam pom yog

Rau cov neeg feem ntau uas muaj tus mob Hughes, cov paib thiab cov tsos mob tuaj yeem tswj hwm tau nrog rau cov ntshav hauv cov ntshav thiab cov tshuaj anticoagulant.

Muaj qee kis uas kev kho mob no tsis pab tau zoo, thiab lwm txoj hauv kev yuav tsum tau siv los tiv thaiv koj cov ntshav txhaws.

Yog tias tsis kho, Hughes syndrome tuaj yeem ua kev puas tsuaj rau koj cov hlab plawv thiab ua rau koj muaj kev pheej hmoo rau lwm yam mob, zoo li kev nchuav menyuam thiab mob stroke. Kev kho mob ntawm Hughes syndrome tag lub neej, vim tias tsis muaj ib txoj hauv kev kho tus mob no.

Yog tias koj muaj ib qho hauv qab no, nrog koj tus kws kho mob tham txog kev sim tus mob Hughes:

  • ntau tshaj ib qho qhia tau tias cov ntshav txhaws uas ua rau muaj teeb meem
  • ib lossis ntau dua kev nchuav menyuam tom qab 10 lub limtiam uas cev xeeb tub
  • peb lossis ntau tshaj kev nchuav menyuam ntxov hauv thawj lub hlis thaum cev xeeb tub

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