Dermatomyositis: nws yog dab tsi, cov tsos mob thiab kev kho mob

Zoo Siab

• Cov tsos mob tseem ceeb
• Yuav kuaj li cas
• Yuav kho li cas

Dermatomyositis yog ib yam mob tsis tshua muaj mob uas cuam tshuam rau cov leeg nqaij thiab tawv nqaij, ua rau cov leeg tsis muaj zog thiab mob nqaij tawv. Nws tshwm sim feem ntau rau cov poj niam thiab muaj ntau dua rau cov neeg laus, tab sis nws tuaj yeem tshwm rau cov neeg tsis tau muaj hnub nyoog 16, raug hu ua menyuam yaus dermatomyositis.

Qee zaum, kab mob dermatomyositis cuam tshuam nrog mob qog noj ntshav, uas tuaj yeem ua lub cim ntawm kev tsim qee yam mob qog nqaij hlav cancer xws li ntsws, mis, ovarian, prostate thiab mob hnyuv loj. Nws kuj tuaj yeem cuam tshuam nrog lwm cov kab mob ntawm kev tiv thaiv kab mob, xws li scleroderma thiab sib xyaw ua ke ntawm cov nqaij mob sib kis. Kuj to taub dab tsi scleroderma yog.

Cov laj thawj ntawm tus kab mob no yog cov keeb tiv thaiv autoimmune, uas lub cev tiv thaiv lub cev tawm tsam cov leeg thiab ua rau daim tawv nqaij mob, thiab, txawm hais tias vim li cas rau cov tshuaj tiv thaiv no tseem tsis tau nkag siab, nws paub tias nws muaj feem xyuam rau caj ces hloov pauv, lossis cuam tshuam los ntawm kev siv qee yam tshuaj noj lossis kab mob kis. Dermatomyositis tsis muaj kev kho kom zoo, thiab yog li ntawd yog mob ntev, txawm li cas los xij, kev kho mob nrog corticosteroids lossis tshuaj tiv thaiv kab mob tuaj yeem pab tswj cov tsos mob tshwm sim.

Cov tsos mob tseem ceeb

Cov tsos mob ntawm dermatomyositis tuaj yeem suav nrog:

• Nqaij ua kom tsis muaj zog, tshwj xeeb tshaj yog nyob rau hauv thaj chaw scapular, pelvic thiab ncauj tsev menyuam, symmetrically thiab nrog kev mob zuj zus ntxiv;
• Cov tsos mob ntawm cov pob lossis me me tso tawm cov tawv nqaij tawv, tshwj xeeb tshaj yog cov pob qij txha ntawm cov ntiv tes, lauj tshib thiab hauv caug, hu ua Gottron cov paib lossis papules;
• Cov pa liab vog rau ntawm daim tawv muag sab saud, hu ua heliotrope;
• Mob tej pob txha thiab o;
• Ua npaws;
• Nkees nkees;
• Nyuaj noj nyuaj;
• Mob plab;
• Ntuav;
• Lub cev yuag.

Feem ntau, cov neeg muaj tus kabmob no tuaj yeem nyuaj rau kev ua txhua hnub xws li sib txuas lawv cov plaub hau, taug kev, nce ntaiv lossis nce lub rooj zaum. Tsis tas li ntawd, cov tsos mob ntawm daim tawv nqaij yuav cuam tshuam nrog lub hnub.

Feem ntau ntawm cov mob hnyav, lossis thaum dermatomyositis tshwm sim koom nrog lwm cov kabmob autoimmune, lwm yam kabmob xws li lub plawv, lub ntsws lossis lub raum yuav cuam tshuam, cuam tshuam rau nws txoj haujlwm thiab ua rau muaj kev phom sij loj.

Yuav kuaj li cas

Kev txheeb xyuas tus mob dermatomyositis yog tsim los ntawm kev ntsuam xyuas cov tsos mob ntawm tus kabmob, kev tshuaj xyuas lub cev thiab kev kuaj mob xws li kev kuaj mob hauv lub cev, kev kuaj mob hauv lub cev lossis kuaj ntshav los kuaj lub cev muaj cov tshuaj uas qhia txog kev puas tsuaj ntawm cov leeg, xws li CPK, DHL lossis AST. cov kev ntsuas, piv txwv.

Tej zaum yuav muaj cov tshuaj tiv thaiv kab mob autoantibodies, piv txwv li cov tshuaj tua kab mob myositis (MSAs), anti-RNP lossis anti MJ, piv txwv. uas tuaj yeem pom hauv cov ntau hauv kev kuaj ntshav.

Txhawm rau kom paub tseeb tias kev kuaj mob, nws tseem tsim nyog rau tus kws kho mob sib txawv ntawm cov tsos mob dermatomyositis los ntawm lwm cov kab mob uas ua rau cov tsos mob zoo sib xws, xws li polymyositis lossis myositis nrog rau lub cev sib xyaw, uas tseem yog cov kab mob ntawm cov leeg. Lwm yam kab mob uas yuav tsum tau txiav txim siab yog myofascitis, necrotizing myositis, polymyalgia rheumatica lossis mob los ntawm kev siv tshuaj, xws li clofibrate, simvastatin lossis amphotericin, piv txwv.

Yuav kho li cas

Kev kho mob ntawm dermatomyositis yog ua tiav raws li cov tsos mob tau nthuav tawm los ntawm cov neeg mob, tab sis feem ntau nws suav nrog kev siv:

• Corticosteroids zoo li Prednisone, raws li lawv txo qhov mob hauv lub cev;
• Kev txhaj tshuaj tiv thaiv kab mob xws li Methotrexate, Azathioprine, Mycophenolate lossis Cyclophosphamide, kom txo tau cov lus teb rau lub cev tsis muaj zog;
• Lwm txoj kev kho mob, piv txwv li Hydroxychloroquine, vim tias lawv muaj txiaj ntsig los daws cov tsos mob dermatological, xws li kev nkag siab mus rau lub teeb, piv txwv li.

Cov kev hais daws no feem ntau coj hauv kev txhaj tshuaj ntau thiab rau lub sijhawm ntev, thiab muaj cov nyhuv ntawm txo qis hauv cov txheej txheem o thiab txo cov tsos mob ntawm tus kab mob. Thaum cov tshuaj no tsis ua haujlwm, lwm txoj hauv kev yog los tswj hwm tib neeg ntawm immunoglobulin.

Nws tseem tuaj yeem ua kev sim kho lub cev, nrog kev tawm dag zog kom rov zoo uas pab txo cov tsos mob thiab zam kev cog lus thiab rov ua dua. Photoprotection tseem tau taw qhia, nrog tshuaj pleev thaiv hnub, los tiv thaiv qhov tawv nqaij ntawm qhov tawv nqaij mob.

Thaum dermatomyositis cuam tshuam nrog mob qog nqaij hlav, txoj kev kho mob uas tsim nyog tshaj plaws yog kho mob qog nqaij hlav, feem ntau ua rau cov tsos mob thiab tus tsos mob tshwm sim ua siab ntev.