Tus Sau: Joan Hall
Hnub Kev Tsim: 27 Lub Ob Hli Ntuj 2021
Hloov Hnub: 3 Tau 2025
Anonim
Inherited Retinal Dystrophies - May 1, 2020
Daim Duab: Inherited Retinal Dystrophies - May 1, 2020

Choroidal dystrophy yog qhov cuam tshuam qhov muag uas cuam tshuam nrog ib txheej ntawm cov hlab ntshav hu ua choroid. Cov hlab ntsha no yog nyob nruab nrab ntawm sclera thiab retina.

Feem ntau, mob choroidal dystrophy yog vim muaj cov gene tsis meej, uas tau dhau los ntawm tsev neeg. Feem ntau nws ua rau txiv neej, pib txij thaum me me los.

Thawj qhov tsos mob yog lub qhov muag pom kev tsis pom kev thiab tsis pom kev thaum tsaus ntuj. Tus kws phais qhov muag uas ua tus tshwj xeeb hauv retina (nraub qaum qhov muag) tuaj yeem txheeb xyuas qhov tsis zoo no.

Cov kev ntsuam xyuas hauv qab no yuav xav tau los ntsuas tus mob:

  • Electroretinography
  • Fluorescein angiography
  • Kev tshuaj ntsuam caj ces

Choroideremia; Gyrate atrophy; Nruab nrab areolar choroidal dystrophy

  • Sab nraud thiab sab hauv lub qhov muag lub cev

Freund KB, Sarraf D, Mieler WF, Yannuzzi LA. Cov roj ntsha chorioretinal pob txha caj qaum. Hauv: Freund KB, Sarraf D, Mieler WF, Yannuzzi LA, eds. Lub Retinal AtlasCov. 2nd ed. Philadelphia, PA: Elsevier; 2017: chap 2.


Grover S, Fishman GA. Choroidal dystrophies. Hauv: Yanoff M, Duker JS, eds. OphthalmologyCov. Thib 5 ed. Philadelphia, PA: Elsevier; 2019: chap 6.16.

Klufas MA, Kiss S. Kev ntsuas qhov muag ntawm daim teb. Hauv: Schachat AP, Sadda SVR, Hinton DR, Wilkinson CP, Wiedemann P, eds. Ryan's RetinaCov. 6 tus ed. Philadelphia, PA: Elsevier; 2018: chap 5.

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