Idiopathic mob ntsws ntsig

Idiopathic pulmonary fibrosis (IPF) muaj caws pliav los yog tuab ntawm lub ntsws yam tsis paub txog yam ua rau.

Cov kws kho mob tsis paub txog dab tsi ua rau IPF lossis vim li cas qee tus neeg thiaj tsim kho. Idiopathic txhais tau tias qhov ua rau tsis paub. Qhov xwm txheej yuav yog vim lub ntsws ua rau tsis paub txog cov tshuaj yeeb lossis raug mob. Cov noob yuav ua lub luag haujlwm hauv kev tsim IPF. Tus mob feem ntau tshwm sim rau cov neeg muaj hnub nyoog 60 thiab 70 xyoo. IPF muaj ntau heev rau txiv neej dua li poj niam.

Thaum koj muaj IPF, koj lub ntsws yuav rov ua pa thiab tawv muag. Qhov no ua rau koj ua pa nyuaj. Hauv cov neeg feem coob, IPF muaj kev phem zuj zus mus ntau lub hlis lossis ob peb xyoos. Hauv lwm tus, IPF cuam tshuam lub sijhawm ntev npaum li cas.

Cov tsos mob tuaj yeem suav nrog ib qho hauv qab no:

• Mob hauv siab (qee zaum)
• Hnoos (feem ntau qhuav)
• Tsis muaj peev xwm yuav nquag npaum li yav dhau los
• Ua tsis taus pa thaum lub sijhawm ua si (qhov tsos mob no kav rau lub hlis lossis xyoo, thiab sijhawm ntev mus kuj yuav tshwm sim thaum so)
• Ntsej muag tsaus muag
• Maj mam yuag yuag

Tus kws khomob yuav kuaj ib ce thiab nug txog koj li keeb kwm kev khomob. Luag yuav nug seb koj puas tau nphav raug asbestos lossis lwm yam tshuaj lom thiab yog tias koj tau haus luam yeeb.

Kev kuaj mob lub cev yuav pom tias koj muaj:

• Lub suab ua pa txawv txav hu ua crackles
• Cov tawv nqaij bluish (cyanosis) nyob ib ncig ntawm lub qhov ncauj lossis rau tes vim muaj cov pa oxygen (nrog rau cov kab mob siab)
• Kev nthuav dav thiab nkhaus ntawm cov rau tes ntiv tes, hu ua clubbing (nrog mob siab heev)

Kev ntsuam xyuas uas pab txheeb xyuas IPF suav nrog cov hauv qab no:

• Bronchoscopy
• Kho siab hauv siab CT scan (HRCT)
• Kev ntsuas hluav taws xob xoo
• Echocardiogram
• Kev ntsuas ntawm cov ntshav oxygen theem (arterial ntshav roj)
• Pulmonary muaj nuj nqi xeem
• 6-feeb taug kev kev xeem
• Kev kuaj mob rau cov kab mob autoimmune xws li mob caj dab, mob pob ntseg, lossis scleroderma
• Qhib lub ntsws (phais) mob mus kuaj

Kuj tsis muaj tshuaj kho tau rau IPF.

Txoj kev kho yog hais txog kev daws cov tsos mob thiab ua mob qeeb:

• Pirfenidone (Esbriet) thiab nintedanib (Ofev) yog ob yam tshuaj uas kho IPF. Lawv yuav pab ua rau lub ntsws qeeb.
• Cov neeg muaj ntshav oxygen tsis txaus yuav xav tau kev pab oxygen hauv tsev.
• Lub ntsws rov zoo yuav kho tsis tau tus kab mob, tab sis nws tuaj yeem pab tib neeg qoj ib ce ua pa nyuaj.

Kev hloov pauv hauv tsev thiab lub neej tuaj yeem pab tswj cov tsos mob ua pa. Yog tias koj lossis ib tug neeg hauv tsev neeg haus luam yeeb, tam sim no yog lub sijhawm txwv.

Kev kho mob ntsws tej zaum yuav raug txiav txim siab rau qee tus neeg nrog IPF siab heev.

Koj tuaj yeem daws kev ntxhov siab kev mob los ntawm koom nrog pab pawg txhawb nqa. Faib qhia rau lwm tus uas muaj kev paub thiab teeb meem ntau yam tuaj yeem pab koj tsis txhob xav tias yog ib leeg.

Xav paub ntau ntxiv thiab txhawb nqa rau cov neeg nrog IPF thiab lawv tsev neeg tuaj yeem nrhiav tau ntawm:

• Pulmonary Fibrosis Foundation - www.pulmonaryfibrosis.org/life-with-pf/Support- Pawg Kawm
• Koom Haum American Miskas - www.lung.org/support-and-community/

IPF tuaj yeem txhim kho lossis nyob ruaj khov rau lub sijhawm ntev nrog lossis tsis kho. Cov neeg feem coob mob heev dua, tab txawm siv tshuaj kho.

Thaum cov tsos mob ua pa hnyav dua, koj thiab koj tus kws kho mob yuav tsum sib tham txog kev kho mob uas ua kom lub neej ntev zog, xws li mob ntsws. Thiab sib tham txog kev npaj saib xyuas ua ntej.

Teeb meem ntawm IPF yuav suav nrog:

• Kev ua haujlwm tsis zoo ntawm cov qe ntshav liab vim cov ntshav oxygen tsis txaus
• Lub ntsws ntsws tawg
• Ntshav siab hauv cov hlab ntsha ntawm lub ntsws
• Kev ua pa tsis ua haujlwm
• Cor pulmonale (sab xis-lub plawv nres)
• Kev Tuag

Hu rau koj lub chaw kho mob yog koj muaj tej yam hauv qab no:

• Ua tsis taus pa uas nyuaj dua, nrawm dua, los yog ntiav (koj ua tsis taus pa ib zaug ntxiv)
• Txo mus tom ntej thaum zaum ua pa zoo
• Nquag mob taub hau
• Tsaug tsaug zog lossis tsis meej pem
• Ua npaws
• Cov hnoos qeev dub thaum koj hnoos
• Xauv ntiv tes lossis tawv nqaij ncig koj cov rau tes

Idiopathic diffuse interstitial pulmonary fibrosis; IPF; Mob ntsws pulmonary; Cryptogenic fibrosing alveolitis; CFA; Fibrosing alveolitis; Feem ntau mob ntsws hnoos qeev; UIP

• Siv cov pa oxygen hauv tsev

• Spirometry
• Xab
• Kev ua pa system

Teb chaws lub plawv, lub ntsws, thiab ntshav lub koom haum lub vev xaib. Idiopathic mob ntsws ntsig. www.nhlbi.nih.gov/health-topics/idiopathic-pulmonary-fibrosis. Nkag mus siv thaum Lub Ib Hlis 13, 2020.

Raghu G, Martinez FJ. Cov mob ntsws interstitial. Hauv: Goldman L, Schafer AI, eds. Goldman-Cecil TshuajCov. 26th ed. Philadelphia, PA: Elsevier; 2020: tshooj 86.

Raghu G, Rochwerg B, Zhang Y, li al. Kev ua haujlwm ntawm ATS / ERS / JRS / ALAT cov kev coj ua hauv kev kho mob: kev kho ntawm idiopathic pulmonary fibrosis. Qhov hloov tshiab ntawm 2011 kev soj ntsuam kev qhia. Am J Respir Crit Care MedCov. 2015; 192 (2): e3-e19. PMID: 26177183 pubmed.ncbi.nlm.nih.gov/26177183/.

Ryu JH, Selman M, Colby TV, King TE. Idiopathic interstitial pneumonias mob ntsws. Hauv: Broaddus VC, Mason RJ, Ernst JD, li al, eds. Murray thiab Nadel Cov Ntawv Phau Ntawv Qhia Txog Cov PaCov. 6 tus ed. Philadelphia, PA: Elsevier Saunders; 2016: chap 63.

Silhan LL, Danoff SK. Tsis yog kev kho mob tsis tseem ceeb rau idiopathic pulmonary fibrosis. Hauv: Collard HR, Richeldi L, eds. Kab Mob Los Ntawm Cov Kab Mob KisCov. Philadelphia, PA: Elsevier; 2018: chap 5.