Goodpasture syndrome: nws yog dab tsi, cov tsos mob, ua rau thiab kho

Zoo Siab

• Cov tsos mob tseem ceeb
• Yuav ua li cas kom paub meej tias kuaj mob
• Cov teeb meem muaj peev xwm
• Yuav kho tus mob li cas

Goodpasture Syndrome yog ib yam kab mob autoimmune tsawg, uas lub cev tiv thaiv lub cev tawm tsam lub raum thiab lub ntsws, feem ntau ua rau cov tsos mob xws li hnoos ntshav, ua pa nyuaj thiab poob ntshav hauv cov zis.

Qhov kev mob nkeeg no tshwm sim vim yog cov khoom tiv thaiv tshuaj tiv thaiv lub hlwb ntawm lub raum thiab lub ntsws. Qee yam uas zoo li ua rau muaj kev pheej hmoo ntawm tus mob no ntau tshaj yog: muaj keeb kwm ntawm tus kab mob thiab tseem haus luam yeeb, muaj kab mob ua pa thiab muaj kev nqus tau cov tshuaj xws li methane lossis propane, piv txwv.

Txoj kev kho yog los ntawm kev siv cov tshuaj xws li immunosuppressants thiab corticosteroids, tab sis nyob rau hauv cov mob hnyav dua, plasmapheresis lossis hemodialysis tej zaum yuav tsim nyog.

Cov tsos mob tseem ceeb

Cov tsos mob tseem ceeb ntawm Goodpasture Syndrome yog:

• Nkees dhau heev;
• Kev hnoos tau ntshav;
• Ua pa nyuaj;
• Mob thaum nqus pa;
• Nce qib ntawm urea hauv cov ntshav;
• Muaj ntshav thiab / lossis ua npuas ncauj hauv cov zis;
• Hlawv thaum tso zis.

Thaum pom cov tsos mob tshwm sim, nws raug nquahu kom nrhiav kev kho sai sai rau kev kuaj mob thiab kev qhia txog kev kho mob uas tsim nyog tshaj plaws, vim tias cov tsos mob yuav mob heev dua yog tias tsis kho tus kab mob thaum ntxov.

Tsis tas li ntawd, lwm cov kab mob yuav muaj cov tsos mob zoo li cov kab mob no, xws li Wegener lub granulomatosis, uas ua rau kev kuaj mob nyuaj. Paub cov tsos mob thiab seb yuav kho Wegener lub granulomatosis.

Yuav ua li cas kom paub meej tias kuaj mob

Txhawm rau soj ntsuam Goodpasture's syndrome, tus kws kho mob yuav tshuaj xyuas koj li keeb kwm kev noj qab haus huv thiab lub sijhawm koj cov tsos mob tshwm sim. Tom qab ntawd, tus kws kho mob tuaj yeem xaj qee qhov kev sim, xws li kuaj ntshav thiab tso zis, txhawm rau txheeb xyuas cov tshuaj tiv thaiv uas ua los ntawm lub cev uas ua rau Goodpasture's syndrome.

xws li lub raum ua haujlwm, uas yog tshem tawm qee qhov me me ntawm lub raum cov ntaub so ntswg, kom pom tias muaj cov cell uas ua rau Goodpasture's syndrome.

Ib qho ntxiv, tus kws kho mob tseem tuaj yeem ua lwm yam kev kuaj mob, xws li lub raum ua haujlwm, uas muaj qhov tshem me me ib feem ntawm lub raum cov ntaub so ntswg uas yuav raug ntsuas hauv chav kuaj mob, txhawm rau saib seb puas muaj cov cell uas ua rau Goodpasture syndrome.

Kev xoo hluav taws xob thiab kev thaij duab xaj xaj kuj tuaj yeem xaj los ntawm koj tus kws kho mob kom kuaj pom kev puas tsuaj rau lub ntsws. Saib cov ntsiab lus ntxiv ntawm yuav ua li cas suav tomography ua.

Cov teeb meem muaj peev xwm

Qhov ua rau ntawm Goodpasture's syndrome yog vim muaj cov tshuaj tiv thaiv GBM uas tawm tsam NC-1 ntu ntawm hom IV collagen hauv lub raum thiab lub ntsws.

Tus mob no tshwm sim rau cov txiv neej ntau dua li poj niam, thaj tsam 20 txog 30 xyoo, thiab cov neeg muaj tawv nqaij tawv. Tsis tas li ntawd, kis tau cov tshuaj xws li tshuaj tua kab, luam yeeb haus luam yeeb, thiab kis los ntawm kab mob yog lwm yam uas ua rau muaj kev pheej hmoo ntawm tus mob tshwm sim, vim lawv tuaj yeem ua rau lub cev tiv thaiv lub hlwb ua mob rau lub ntsws thiab lub raum.

Yuav kho tus mob li cas

Kev kho ntawm Goodpasture's Syndrome feem ntau yog coj hauv tsev kho mob thiab ua raws li kev siv tshuaj tiv thaiv kab mob thiab corticosteroids, uas tiv thaiv lub cev tiv thaiv lub cev los ntawm kev rhuav tshem lub raum thiab lub ntsws.

Muaj qee kis, kev kho mob los ntawm plasmapheresis yog qhia, uas yog tus txheej txheem uas lim cov ntshav thiab cais cov tshuaj tiv thaiv uas ua mob rau lub raum thiab lub ntsws. Yog tias lub raum tau cuam tshuam loj heev, kev hloov kho mob hauv lub raum lossis lub raum yuav tsum tau ua. Zoo nkag siab dab tsi plasmapheresis yog thiab nws yuav ua li cas.